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SURF1 [mitochondrial inner membrane]
Stable Identifier
R-HSA-5336159
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Surfeit locus protein 1, SURF1_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex IV assembly (Homo sapiens)
MT-CO1 and MT-CO2 complexes associate, installing heme moieties (Homo sapiens)
MT-CO1:Cu2+:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
holo-MT-CO1,2 complex [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
MT-CO1 mRNA is translated (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
MT-CO3, COX6A,B,7A and NDUFA4 bind to holo-MT-CO1,2 complex (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
holo-MT-CO1,2 complex [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
Metallochaperone inserts Cu2+ into MT-CO1 (Homo sapiens)
MT-CO1:Cu2+:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
Nascent MT-CO1 binds to MITRAC, Mg2+, PE, CL (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
TIMM21 carries COX4, COX5A, COX6C to MT-CO1:MITRAC (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SURF1 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q15526 SURF1
Gene Names
SURF1, SURF-1
Chain
chain:1-300
Reference Genes
BioGPS Gene:6834 SURF1
COSMIC (genes):SURF1 SURF1
CTD Gene:6834 SURF1
dbSNP Gene:6834 SURF1
ENSEMBL:ENSG00000148290 SURF1
HGNC:11474 SURF1
KEGG:hsa:6834 SURF1
Monarch:6834 SURF1
NCBI Gene:6834 SURF1
OMIM:185620 SURF1
UCSC:Q15526 SURF1
Reference Transcript
RefSeq:NM_001280787.1 SURF1
RefSeq:NM_003172.3 SURF1
Other Identifiers
11721536_a_at
17099498
204295_PM_at
204295_at
217646_PM_at
217646_at
2691617
3228653
3228654
3228655
3228657
3228659
3228660
3228661
3228662
3228664
3228666
3228667
3228668
3228669
3228670
3228671
3228672
3228673
3361469
35646_at
4051946
4051947
4051948
4051950
4051952
4051953
4051954
4051955
4051957
4051959
4051960
4051961
4051962
4051963
4051964
4051965
6834
8164896
A_23_P20648
A_23_P300479
A_24_P453544
A_33_P3292560
GE60397
GO:0003824
GO:0004129
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0006091
GO:0008535
GO:0009060
GO:0016020
GO:0016491
GO:0033617
GO:0043226
GO:0055085
GO:0065003
GO:0098803
GO:1902600
HMNXSV003007952
HMNXSV003036919
Hs.257150.0.A1_3p_at
ILMN_1663407
PH_hs_0019792
PH_hs_0033280
TC09001687.hg
Z35093_at
g4507318_3p_at
Participates
as a component of
MITRAC [mitochondrial inner membrane] (Homo sapiens)
Inferred To
Surf1 [mitochondrial inner membrane]
(Drosophila melanogaster)
Surf1 [mitochondrial inner membrane]
(Mus musculus)
Surf1 [mitochondrial inner membrane]
(Rattus norvegicus)
sft-1 [mitochondrial inner membrane]
(Caenorhabditis elegans)
SURF1 [mitochondrial inner membrane]
(Bos taurus)
SURF1 [mitochondrial inner membrane]
(Canis familiaris)
SURF1 [mitochondrial inner membrane]
(Sus scrofa)
Cross References
ENSEMBL
ENSP00000361042
,
ENSP00000487158
,
ENST00000371974
,
ENST00000626663
OpenTargets
ENSG00000148290
HPA
ENSG00000148290-SURF1
PRO
Q15526
Pharos - Targets
Q15526
Orphanet
SURF1
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