Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
ADAMTS3 [endoplasmic reticulum lumen]
Stable Identifier
R-HSA-5173135
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
endoplasmic reticulum lumen
Synonyms
A disintegrin and metalloproteinase with thrombospondin motifs 3, ATS3_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
O-linked glycosylation (Homo sapiens)
O-glycosylation of TSR domain-containing proteins (Homo sapiens)
POFUT2 transfers fucose to TSR domain-containing proteins (Homo sapiens)
POFUT2 substrates [endoplasmic reticulum lumen] (Homo sapiens)
ADAMTS3 [endoplasmic reticulum lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:O15072 ADAMTS3
Gene Names
ADAMTS3, KIAA0366
Chain
signal peptide:1-20, propeptide:21-249, chain:250-1205
Reference Genes
BioGPS Gene:9508 ADAMTS3
COSMIC (genes):ADAMTS3 ADAMTS3
CTD Gene:9508 ADAMTS3
dbSNP Gene:9508 ADAMTS3
ENSEMBL:ENSG00000156140 ADAMTS3
HGNC:219 ADAMTS3
Monarch:9508 ADAMTS3
NCBI Gene:9508 ADAMTS3
OMIM:605011 ADAMTS3
UCSC:O15072 ADAMTS3
Reference Transcript
RefSeq:NM_014243.2 ADAMTS3
Other Identifiers
11731357_a_at
11731358_at
11762267_at
16976706
214913_PM_at
214913_at
2772880
2772881
2772882
2772883
2772884
2772885
2772886
2772887
2772888
2772889
2772890
2772894
2772895
2772896
2772897
2772898
2772899
2772900
2772901
2772902
2772903
2772904
2772906
2772909
2772918
2772931
2772936
2772937
2772938
2772939
36269_at
8100870
9508
A_23_P144521
A_24_P140405
GE53084
GO:0001701
GO:0003824
GO:0004175
GO:0004222
GO:0005515
GO:0005576
GO:0005615
GO:0006508
GO:0008201
GO:0008233
GO:0008237
GO:0008270
GO:0010573
GO:0016485
GO:0016787
GO:0030198
GO:0030199
GO:0030312
GO:0030574
GO:0031012
GO:0032964
GO:0043226
GO:0046872
GO:0048856
GO:0051604
GO:0062023
GO:0070062
GO:0097435
GO:0140096
GO:1900748
HMNXSV003020666
Hs.27916.0.S1_3p_at
ILMN_1703803
PH_hs_0026899
TC04001277.hg
Participates
as a candidate of
POFUT2 substrates [endoplasmic reticulum lumen] (Homo sapiens)
Other forms of this molecule
ADAMTS3 [extracellular region]
glc-fuc-ADAMTS3 [endoplasmic reticulum lumen]
O-fuc-ADAMTS3 [endoplasmic reticulum lumen]
Inferred To
rsc22 [endoplasmic reticulum lumen]
(Dictyostelium discoideum)
ADAMTS3 [endoplasmic reticulum lumen]
(Bos taurus)
ADAMTS3 [endoplasmic reticulum lumen]
(Canis familiaris)
ADAMTS3 [endoplasmic reticulum lumen]
(Gallus gallus)
ADAMTS3 [endoplasmic reticulum lumen]
(Mus musculus)
ADAMTS3 [endoplasmic reticulum lumen]
(Rattus norvegicus)
ADAMTS3 [endoplasmic reticulum lumen]
(Sus scrofa)
ADAMTS3 [endoplasmic reticulum lumen]
(Xenopus tropicalis)
Cross References
Guide to Pharmacology - Targets
1676
ENSEMBL
ENSP00000286657
,
ENST00000286657
OpenTargets
ENSG00000156140
HPA
ENSG00000156140-ADAMTS3
PRO
O15072
Pharos - Targets
O15072
GlyGen
O15072
Orphanet
ADAMTS3
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text