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ACADVL [mitochondrial matrix]
Stable Identifier
R-HSA-49495
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Acyl-CoA dehydrogenase, very-long-chain specific, mitochondrial precursor , VLCAD
Locations in the PathwayBrowser
Expand all
Cellular responses to stimuli (Homo sapiens)
Cellular responses to stress (Homo sapiens)
Unfolded Protein Response (UPR) (Homo sapiens)
IRE1alpha activates chaperones (Homo sapiens)
XBP1(S) activates chaperone genes (Homo sapiens)
Expression of ACADVL (Homo sapiens)
ACADVL [mitochondrial matrix] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Homo sapiens)
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Homo sapiens)
palmitoyl-CoA+FAD<=>trans-Hexadec-2-enoyl-CoA+FADH2 (Homo sapiens)
ACADVL dimer [mitochondrial matrix] (Homo sapiens)
ACADVL [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:P49748 ACADVL
Gene Names
ACADVL, VLCAD
Chain
transit peptide:1-40, chain:41-655
Reference Genes
BioGPS Gene:37 ACADVL
COSMIC (genes):ACADVL ACADVL
CTD Gene:37 ACADVL
dbSNP Gene:37 ACADVL
ENSEMBL:ENSG00000072778 ACADVL
HGNC:92 ACADVL
KEGG:hsa:37 ACADVL
Monarch:37 ACADVL
NCBI Gene:37 ACADVL
OMIM:609575 ACADVL
UCSC:P49748 ACADVL
Reference Transcript
RefSeq:NM_000018.3 ACADVL
RefSeq:NM_001033859.2 ACADVL
RefSeq:NM_001270447.1 ACADVL
Other Identifiers
11744255_a_at
11745736_a_at
11745737_x_at
16830302
200710_3p_at
200710_PM_at
200710_at
37
3708308
3708309
3708310
3708311
3708312
3708313
3708314
3708315
3708316
3708317
3708318
3708319
3708320
3708321
3708322
3708323
3708324
3708325
3708326
3708327
3708328
3708329
3708330
3708331
3708332
3708333
3708334
3708335
3708336
3708337
3708338
3708339
3708340
3708341
3708342
3708343
3708344
3708345
3708346
3708347
3708348
3708349
3708350
3708351
38376_at
8004271
87468_at
A_14_P129937
A_23_P207650
D43682_s_at
GE62165
GO:0000062
GO:0001659
GO:0003824
GO:0003995
GO:0004466
GO:0005515
GO:0005654
GO:0005730
GO:0005739
GO:0005743
GO:0005759
GO:0006091
GO:0006629
GO:0006631
GO:0008289
GO:0009062
GO:0009409
GO:0015980
GO:0016491
GO:0016627
GO:0017099
GO:0030154
GO:0030855
GO:0031966
GO:0033539
GO:0042645
GO:0042802
GO:0043226
GO:0045717
GO:0046322
GO:0050660
GO:0090181
HMNXSV003019355
ILMN_1806408
ILMN_2263466
ILMN_2352009
PH_hs_0020653
TC17000085.hg
g4557234_3p_at
g4557234_3p_s_at
Participates
as an output of
Expression of ACADVL (Homo sapiens)
as a component of
ACADVL dimer [mitochondrial matrix] (Homo sapiens)
Inferred To
Acadvl [mitochondrial matrix]
(Drosophila melanogaster)
acdh-12 [mitochondrial matrix]
(Caenorhabditis elegans)
ACADVL [mitochondrial matrix]
(Bos taurus)
ACADVL [mitochondrial matrix]
(Canis familiaris)
ACADVL [mitochondrial matrix]
(Mus musculus)
ACADVL [mitochondrial matrix]
(Rattus norvegicus)
ACADVL [mitochondrial matrix]
(Sus scrofa)
acadvl [mitochondrial matrix]
(Danio rerio)
Cross References
ENSEMBL
ENSP00000438689
,
ENST00000543245
,
ENST00000356839
,
ENST00000350303
,
ENSP00000349297
,
ENSP00000344152
OpenTargets
ENSG00000072778
HPA
ENSG00000072778-ACADVL
PRO
P49748
Pharos - Targets
P49748
GlyGen
P49748
Orphanet
ACADVL
HMDB Protein
HMDBP08259
PDB
2UXW
,
3B96
,
7S7G
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q53T94 TAF1B
2
TAF1B [nucleoplasm]
(R-HSA-73691)
Ac-TAF1B [nucleoplasm]
(R-HSA-5138530)
0.556
3
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