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PPA2 [mitochondrial matrix]
Stable Identifier
R-HSA-449918
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
pyrophosphatase (inorganic) 2, Inorganic pyrophosphatase 2, mitochondrial
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Pyrophosphate hydrolysis (Homo sapiens)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Homo sapiens)
PPA2 dimer [mitochondrial matrix] (Homo sapiens)
PPA2 [mitochondrial matrix] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Translation (Homo sapiens)
tRNA Aminoacylation (Homo sapiens)
Mitochondrial tRNA aminoacylation (Homo sapiens)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Homo sapiens)
PPA2 dimer [mitochondrial matrix] (Homo sapiens)
PPA2 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9H2U2 PPA2
Gene Names
PPA2, HSPC124
Chain
transit peptide:1-32, chain:33-334
Reference Genes
BioGPS Gene:27068 PPA2
COSMIC (genes):PPA2 PPA2
CTD Gene:27068 PPA2
dbSNP Gene:27068 PPA2
ENSEMBL:ENSG00000138777 PPA2
HGNC:28883 PPA2
KEGG Gene (Homo sapiens):27068 PPA2
Monarch:27068 PPA2
NCBI Gene:27068 PPA2
OMIM:609988 PPA2
UCSC:Q9H2U2 PPA2
Reference Transcript
RefSeq:NM_006903.4 PPA2
RefSeq:NM_176869.2 PPA2
RefSeq:NM_176866.2 PPA2
RefSeq:NM_176867.3 PPA2
Other Identifiers
0002190110
0005700358
11722229_a_at
11731853_x_at
11740899_x_at
11741824_x_at
11747013_a_at
1556285_s_at
16978661
220741_s_at
27068
2780543
2780544
2780545
2780546
2780548
2780557
2780559
2780560
2780565
2780578
2780581
2780590
2780593
2780595
2780598
2780610
2780611
43512_s_at
43514_at
49061_at
8102141
A_24_P214625
GE55508
GO:0000287
GO:0003674
GO:0004427
GO:0004722
GO:0005515
GO:0005575
GO:0005622
GO:0005737
GO:0005739
GO:0005759
GO:0005829
GO:0006399
GO:0006412
GO:0006418
GO:0006464
GO:0006470
GO:0006520
GO:0006796
GO:0008150
GO:0009058
GO:0016787
GO:0016791
GO:0034641
GO:0043167
GO:0043226
GO:0044281
GO:0046872
GO:0051881
GO:0071344
HMNXSV003034069
Hs2.384630.1.A1_3p_s_at
ILMN_1687785
ILMN_1755041
ILMN_2342455
PH_hs_0019753
TC04002662.hg
g13491177_3p_a_at
Participates
as a component of
PPA2 dimer [mitochondrial matrix] (Homo sapiens)
Inferred To
PPA2 [mitochondrial matrix]
(Bos taurus)
PPA2 [mitochondrial matrix]
(Canis familiaris)
PPA2 [mitochondrial matrix]
(Plasmodium falciparum)
PPA2 [mitochondrial matrix]
(Sus scrofa)
Nurf-38 [mitochondrial matrix]
(Drosophila melanogaster)
IPP1 [mitochondrial matrix]
(Saccharomyces cerevisiae)
Ppa2 [mitochondrial matrix]
(Mus musculus)
Ppa2 [mitochondrial matrix]
(Rattus norvegicus)
PPA1 [mitochondrial matrix]
(Gallus gallus)
Homologues of PPA2 [mitochondrial matrix]
(Plasmodium falciparum)
ppa1 [mitochondrial matrix]
(Dictyostelium discoideum)
ppa1 [mitochondrial matrix]
(Schizosaccharomyces pombe)
ppa1 [mitochondrial matrix]
(Xenopus tropicalis)
pyp-1 [mitochondrial matrix]
(Caenorhabditis elegans)
ppa1b [mitochondrial matrix]
(Danio rerio)
Cross References
RefSeq
NP_789845.1
,
NP_789843.2
,
NP_789842.2
,
NP_008834.3
OpenTargets
ENSG00000138777
GeneCards
Q9H2U2
HPA
ENSG00000138777-PPA2
Ensembl
ENSP00000313061
,
ENST00000432483
,
ENSP00000343885
,
ENSP00000389957
,
ENST00000341695
,
ENST00000354147
,
ENSG00000138777
,
ENST00000348706
,
ENSP00000340352
PRO
Q9H2U2
Pharos - Targets
Q9H2U2
GlyGen
Q9H2U2
Orphanet
25189
HMDB Protein
HMDBP05093
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