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PPA2 [mitochondrial matrix]
Stable Identifier
R-HSA-449918
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
pyrophosphatase (inorganic) 2, Inorganic pyrophosphatase 2, mitochondrial
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Pyrophosphate hydrolysis (Homo sapiens)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Homo sapiens)
PPA2 dimer [mitochondrial matrix] (Homo sapiens)
PPA2 [mitochondrial matrix] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Translation (Homo sapiens)
tRNA Aminoacylation (Homo sapiens)
Mitochondrial tRNA aminoacylation (Homo sapiens)
pyrophosphate + H2O => 2 orthophosphate [mitochondrial] (Homo sapiens)
PPA2 dimer [mitochondrial matrix] (Homo sapiens)
PPA2 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9H2U2 PPA2
Gene Names
PPA2, HSPC124
Chain
transit peptide:1-32, chain:33-334
Reference Genes
BioGPS Gene:27068 Q9H2U23
COSMIC (genes):PPA2 PPA2
CTD Gene:27068 Q9H2U23
dbSNP Gene:27068 PPA2
ENSEMBL:ENSG00000138777 PPA2
HGNC:28883 Q9H2U23
KEGG:hsa:27068 Q9H2U23
Monarch:27068 Q9H2U23
NCBI Gene:27068 Q9H2U23
OMIM:609988 Q9H2U23
UCSC:Q9H2U2 Q9H2U23
Reference Transcript
RefSeq:NM_176867.3 Q9H2U23
RefSeq:NM_176866.2 Q9H2U23
RefSeq:NM_176869.3 Q9H2U23
RefSeq:NM_006903.4 Q9H2U23
Participates
as a component of
PPA2 dimer [mitochondrial matrix] (Homo sapiens)
Inferred To
PPA2 [mitochondrial matrix]
(Bos taurus)
PPA2 [mitochondrial matrix]
(Canis familiaris)
PPA2 [mitochondrial matrix]
(Gallus gallus)
PPA2 [mitochondrial matrix]
(Plasmodium falciparum)
PPA2 [mitochondrial matrix]
(Sus scrofa)
Nurf-38 [mitochondrial matrix]
(Drosophila melanogaster)
IPP1 [mitochondrial matrix]
(Saccharomyces cerevisiae)
Ppa2 [mitochondrial matrix]
(Mus musculus)
Ppa2 [mitochondrial matrix]
(Rattus norvegicus)
ppa2 [mitochondrial matrix]
(Xenopus tropicalis)
Homologues of PPA2 [mitochondrial matrix]
(Plasmodium falciparum)
ppa1 [mitochondrial matrix]
(Dictyostelium discoideum)
ppa1 [mitochondrial matrix]
(Schizosaccharomyces pombe)
pyp-1 [mitochondrial matrix]
(Caenorhabditis elegans)
ppa1b [mitochondrial matrix]
(Danio rerio)
Cross References
RefSeq
NP_789843.2
,
NP_789842.2
,
NP_789845.1
,
NP_008834.3
ENSEMBL
ENSP00000343885
,
ENSP00000340352
,
ENST00000432483
,
ENSP00000313061
,
ENST00000341695
,
ENST00000354147
,
ENST00000348706
,
ENSG00000138777
,
ENSP00000389957
OpenTargets
ENSG00000138777
GeneCards
PPA2
HPA
ENSG00000138777-PPA2
PRO
Q9H2U2
Pharos - Targets
Q9H2U2
GlyGen
Q9H2U2
HMDB Protein
HMDBP05093
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