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polyGlc-GYG2:GYS2-a tetramer [cytosol]
Stable Identifier
R-HSA-3322056
Type
Complex
Species
Homo sapiens
Compartment
cytosol
GO Cellular Component
glycogen granule
(0042587)
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of carbohydrate metabolism (Homo sapiens)
Glycogen storage diseases (Homo sapiens)
Glycogen storage disease type IV (GBE1) (Homo sapiens)
Defective GBE1 does not catalyze branch formation in growing glycogen chains (liver) (Homo sapiens)
polyGlc-GYG2:GYS2-a tetramer [cytosol] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycogen metabolism (Homo sapiens)
Glycogen synthesis (Homo sapiens)
GBE1 catalyzes branch formation in polyGlc-GYG2 complexed with GYS2-a (Homo sapiens)
polyGlc-GYG2:GYS2-a tetramer [cytosol] (Homo sapiens)
GYS2 catalyzes the polyglucosylation of oligoGlc-GYG2 (Homo sapiens)
polyGlc-GYG2:GYS2-a tetramer [cytosol] (Homo sapiens)
Participants
components
x 2
GYS2 [cytosol]
(Homo sapiens)
Mg2+ [cytosol]
x 2
poly((1,4)-alpha-glucosyl)GYG2 [cytosol]
(Homo sapiens)
Participates
as an input of
Defective GBE1 does not catalyze branch formation in growing glycogen chains (liver) (Homo sapiens)
GBE1 catalyzes branch formation in polyGlc-GYG2 complexed with GYS2-a (Homo sapiens)
as an output of
GYS2 catalyzes the polyglucosylation of oligoGlc-GYG2 (Homo sapiens)
Inferred To
polyGlc-GYG2:GYS2-a tetramer [cytosol]
(Bos taurus)
polyGlc-GYG2:GYS2-a tetramer [cytosol]
(Caenorhabditis elegans)
polyGlc-GYG2:GYS2-a tetramer [cytosol]
(Canis familiaris)
polyGlc-GYG2:GYS2-a tetramer [cytosol]
(Dictyostelium discoideum)
polyGlc-GYG2:GYS2-a tetramer [cytosol]
(Drosophila melanogaster)
polyGlc-GYG2:GYS2-a tetramer [cytosol]
(Gallus gallus)
polyGlc-GYG2:GYS2-a tetramer [cytosol]
(Saccharomyces cerevisiae)
polyGlc-GYG2:GYS2-a tetramer [cytosol]
(Sus scrofa)
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