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2xMMAA [mitochondrial matrix]
Stable Identifier
R-HSA-3159270
Type
Complex
Species
Homo sapiens
Compartment
mitochondrial matrix
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of mitochondrial beta oxidation (Homo sapiens)
Diseases of propionyl-CoA catabolism (Homo sapiens)
Defective MUT causes MMAM (Homo sapiens)
Defective MUT does not isomerise L-MM-CoA to SUCC-CoA (Homo sapiens)
2xMMAA:mutant MUT:AdoCbl [mitochondrial matrix] (Homo sapiens)
2xMMAA [mitochondrial matrix] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
Propionyl-CoA catabolism (Homo sapiens)
MUT isomerises L-MM-CoA to SUCC-CoA (Homo sapiens)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Homo sapiens)
2xMMAA:2xMUT [mitochondrial matrix] (Homo sapiens)
2xMMAA [mitochondrial matrix] (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of water-soluble vitamins and cofactors (Homo sapiens)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Homo sapiens)
Cobalamin (Cbl) metabolism (Homo sapiens)
MMAA:MUT binds AdoCbl (Homo sapiens)
2xMMAA:2xMUT [mitochondrial matrix] (Homo sapiens)
2xMMAA [mitochondrial matrix] (Homo sapiens)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Homo sapiens)
2xMMAA:2xMUT [mitochondrial matrix] (Homo sapiens)
2xMMAA [mitochondrial matrix] (Homo sapiens)
Participants
components
x 2
MMAA [mitochondrial matrix]
(Homo sapiens)
Participates
as a component of
2xMMAA:mutant MUT:AdoCbl [mitochondrial matrix] (Homo sapiens)
2xMMAA:2xMUT [mitochondrial matrix] (Homo sapiens)
Inferred To
2xMMAA [mitochondrial matrix]
(Bos taurus)
2xMMAA [mitochondrial matrix]
(Caenorhabditis elegans)
2xMMAA [mitochondrial matrix]
(Canis familiaris)
2xMMAA [mitochondrial matrix]
(Danio rerio)
2xMMAA [mitochondrial matrix]
(Gallus gallus)
2xMMAA [mitochondrial matrix]
(Mus musculus)
2xMMAA [mitochondrial matrix]
(Rattus norvegicus)
2xMMAA [mitochondrial matrix]
(Sus scrofa)
2xMMAA [mitochondrial matrix]
(Xenopus tropicalis)
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