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PCCA:PCCB [cytosol]
Stable Identifier
R-HSA-2993807
Type
Complex
Species
Homo sapiens
Compartment
cytosol
Synonyms
propionyl-CoA carboxylase protomer
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Defects in vitamin and cofactor metabolism (Homo sapiens)
Defects in biotin (Btn) metabolism (Homo sapiens)
Defective HLCS causes multiple carboxylase deficiency (Homo sapiens)
Defective HLCS does not biotinylate 6x(PCCA:PCCB) (Homo sapiens)
6x(PCCA:PCCB) [cytosol] (Homo sapiens)
PCCA:PCCB [cytosol] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of water-soluble vitamins and cofactors (Homo sapiens)
Biotin transport and metabolism (Homo sapiens)
HLCS biotinylates 6x(PCCA:PCCB) (Homo sapiens)
6x(PCCA:PCCB) [cytosol] (Homo sapiens)
PCCA:PCCB [cytosol] (Homo sapiens)
Literature References
PubMed ID
Title
Journal
Year
The Metabolic and Molecular Bases of Inherited Disease, 8th ed
Beaudet, AL
,
Scriver, CR
,
Sly, WS
,
Valle, D
2001
Participants
components
PCCA [cytosol]
(Homo sapiens)
PCCB [cytosol]
(Homo sapiens)
Participates
as a component of
6x(PCCA:PCCB) [cytosol] (Homo sapiens)
Inferred To
PCCA:PCCB [cytosol]
(Bos taurus)
PCCA:PCCB [cytosol]
(Caenorhabditis elegans)
PCCA:PCCB [cytosol]
(Canis familiaris)
PCCA:PCCB [cytosol]
(Danio rerio)
PCCA:PCCB [cytosol]
(Dictyostelium discoideum)
PCCA:PCCB [cytosol]
(Gallus gallus)
PCCA:PCCB [cytosol]
(Mus musculus)
PCCA:PCCB [cytosol]
(Rattus norvegicus)
PCCA:PCCB [cytosol]
(Sus scrofa)
PCCA:PCCB [cytosol]
(Xenopus tropicalis)
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