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COQ7 [mitochondrial inner membrane]
Stable Identifier
R-HSA-2162218
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Ubiquinone biosynthesis protein COQ7 homolog, COQ7_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
COQ3 methylates DHDB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ7 [mitochondrial inner membrane] (Homo sapiens)
COQ3 methylates DeMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ7 [mitochondrial inner membrane] (Homo sapiens)
COQ4 decarboxylates MHDB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ7 [mitochondrial inner membrane] (Homo sapiens)
COQ5 methylates MDMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ7 [mitochondrial inner membrane] (Homo sapiens)
COQ6 hydroxylates DHB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ7 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ7 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ7 [mitochondrial inner membrane] (Homo sapiens)
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ7 [mitochondrial inner membrane] (Homo sapiens)
COQ8A,B:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
COQ7 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q99807 COQ7
Gene Names
COQ7
Chain
transit peptide:1-35, chain:36-217
Reference Genes
BioGPS Gene:10229 COQ7
COSMIC (genes):COQ7 COQ7
CTD Gene:10229 COQ7
dbSNP Gene:10229 COQ7
ENSEMBL:ENSG00000167186 COQ7
HGNC:2244 COQ7
KEGG:hsa:10229 COQ7
Monarch:10229 COQ7
NCBI Gene:10229 COQ7
OMIM:601683 COQ7
UCSC:Q99807 COQ7
Reference Transcript
RefSeq:NM_016138.4 COQ7
RefSeq:XM_047433495.1 COQ7
RefSeq:NM_001370494.1 COQ7
RefSeq:XM_047433496.1 COQ7
RefSeq:NM_001190983.2 COQ7
RefSeq:NM_001370493.1 COQ7
RefSeq:NM_001370492.1 COQ7
RefSeq:XM_047433494.1 COQ7
Other Identifiers
10229
11753575_at
16816408
209745_PM_at
209745_at
209746_PM_s_at
209746_s_at
210820_PM_x_at
210820_x_at
35385_at
3650803
3650804
3650805
3650806
3650807
3650808
3650809
3650810
3650811
3650812
3650813
3650814
3650816
3650817
3650818
3650819
3650820
3650821
3650822
3650823
3650824
3650825
43996_at
44848_at
59469_f_at
75727_at
7993608
A_23_P152322
A_24_P398972
GE79621
GO:0000122
GO:0003682
GO:0003824
GO:0004497
GO:0005515
GO:0005634
GO:0005694
GO:0005739
GO:0005743
GO:0006355
GO:0006744
GO:0008340
GO:0008682
GO:0010468
GO:0016020
GO:0016491
GO:0016709
GO:0031314
GO:0043226
GO:0045944
GO:0046872
GO:0110142
GO:0160224
GO:2000377
HMNXSV003004248
Hs.157113.0.S2_3p_at
ILMN_1689070
PH_hs_0009500
PH_hs_0040338
TC16000209.hg
g3811294_3p_a_at
Participates
as a component of
COQ7:Fe2+ [mitochondrial inner membrane] (Homo sapiens)
Inferred To
coq7 [mitochondrial inner membrane]
(Danio rerio)
coq7 [mitochondrial inner membrane]
(Dictyostelium discoideum)
coq7 [mitochondrial inner membrane]
(Schizosaccharomyces pombe)
coq7 [mitochondrial inner membrane]
(Xenopus tropicalis)
clk-1 [mitochondrial inner membrane]
(Caenorhabditis elegans)
COQ7 [mitochondrial inner membrane]
(Bos taurus)
COQ7 [mitochondrial inner membrane]
(Canis familiaris)
COQ7 [mitochondrial inner membrane]
(Gallus gallus)
COQ7 [mitochondrial inner membrane]
(Sus scrofa)
Coq7 [mitochondrial inner membrane]
(Drosophila melanogaster)
Coq7 [mitochondrial inner membrane]
(Mus musculus)
Coq7 [mitochondrial inner membrane]
(Rattus norvegicus)
CAT5 [mitochondrial inner membrane]
(Saccharomyces cerevisiae)
Cross References
RefSeq
XP_047289450.1
,
NP_001357423.1
,
NP_001357421.1
,
NP_001357422.1
,
NP_057222.2
,
XP_047289451.1
,
XP_047289452.1
,
NP_001177912.1
ENSEMBL
ENSG00000167186
,
ENST00000568985
,
ENSP00000456734
,
ENSP00000322316
,
ENSP00000442923
,
ENST00000321998
,
ENST00000544894
OpenTargets
ENSG00000167186
IntEnz
1.14.13.253
GeneCards
COQ7
HPA
ENSG00000167186-COQ7
PRO
Q99807
Pharos - Targets
Q99807
Orphanet
COQ7
HMDB Protein
HMDBP01736
PDB
7SSP
,
7SSS
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