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COQ3 [mitochondrial inner membrane]
Stable Identifier
R-HSA-2162206
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
COQ3(86-369), Hexaprenyldihydroxybenzoate methyltransferase, mitochondrial ecNumber2.1.1.114/ecNumber, COQ3_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
COQ3 methylates DHDB (Homo sapiens)
COQ3 [mitochondrial inner membrane] (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ3 [mitochondrial inner membrane] (Homo sapiens)
COQ3 methylates DeMQ10H2 (Homo sapiens)
COQ3 [mitochondrial inner membrane] (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ3 [mitochondrial inner membrane] (Homo sapiens)
COQ4 decarboxylates MHDB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ3 [mitochondrial inner membrane] (Homo sapiens)
COQ5 methylates MDMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ3 [mitochondrial inner membrane] (Homo sapiens)
COQ6 hydroxylates DHB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ3 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ3 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9NZJ6 COQ3
Gene Names
COQ3, UG0215E05
Chain
transit peptide:1-85, chain:86-369
Reference Genes
BioGPS Gene:51805 COQ3
COSMIC (genes):COQ3 COQ3
CTD Gene:51805 COQ3
dbSNP Gene:51805 COQ3
ENSEMBL:ENSG00000132423 COQ3
HGNC:18175 COQ3
KEGG:hsa:51805 COQ3
Monarch:51805 COQ3
NCBI Gene:51805 COQ3
OMIM:605196 COQ3
UCSC:Q9NZJ6 COQ3
Reference Transcript
RefSeq:NM_017421.3 COQ3
Other Identifiers
11728741_at
17021911
221227_PM_x_at
221227_x_at
223515_3p_s_at
223515_PM_s_at
223515_s_at
2966233
2966234
2966235
2966236
2966237
2966238
2966240
2966241
2966242
2966245
2966246
2966249
2966251
2966252
51805
8128383
88452_at
A_23_P111228
A_33_P3221843
GE58748
GO:0003824
GO:0005515
GO:0005739
GO:0005743
GO:0005975
GO:0006071
GO:0006744
GO:0008168
GO:0008171
GO:0010420
GO:0016740
GO:0031314
GO:0032194
GO:0032259
GO:0043226
GO:0061542
GO:0110142
HMNXSV003026955
HMNXSV003050011
ILMN_1801378
PH_hs_0015438
TC06001963.hg
g12052970_3p_at
g12052970_3p_s_at
Participates
as a component of
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
Inferred To
COQ3 [mitochondrial inner membrane]
(Bos taurus)
COQ3 [mitochondrial inner membrane]
(Caenorhabditis elegans)
COQ3 [mitochondrial inner membrane]
(Canis familiaris)
COQ3 [mitochondrial inner membrane]
(Danio rerio)
COQ3 [mitochondrial inner membrane]
(Dictyostelium discoideum)
COQ3 [mitochondrial inner membrane]
(Drosophila melanogaster)
COQ3 [mitochondrial inner membrane]
(Gallus gallus)
COQ3 [mitochondrial inner membrane]
(Mus musculus)
COQ3 [mitochondrial inner membrane]
(Rattus norvegicus)
COQ3 [mitochondrial inner membrane]
(Saccharomyces cerevisiae)
COQ3 [mitochondrial inner membrane]
(Schizosaccharomyces pombe)
COQ3 [mitochondrial inner membrane]
(Sus scrofa)
COQ3 [mitochondrial inner membrane]
(Xenopus tropicalis)
Cross References
RefSeq
NP_059117.3
ENSEMBL
ENSP00000254759
,
ENST00000254759
OpenTargets
ENSG00000132423
HPA
ENSG00000132423-COQ3
PRO
Q9NZJ6
Pharos - Targets
Q9NZJ6
GlyGen
Q9NZJ6
HMDB Protein
HMDBP00417
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P49638 TTPA
1
TTPA [cytosol]
(R-HSA-2980979)
0.556
3
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