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COQ6 [mitochondrial inner membrane]
Stable Identifier
R-HSA-2162200
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Ubiquinone biosynthesis monooxygenase COQ6 ecNumber1.14.13.-/ecNumber, COQ6_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
DHB is hydroxylated to DHDB by COQ6 (Homo sapiens)
COQ6:FAD [mitochondrial inner membrane] (Homo sapiens)
COQ6 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9Y2Z9 COQ6
Gene Names
COQ6, CGI-10
Chain
transit peptide:1-28, chain:29-468
Reference Genes
BioGPS Gene:51004 COQ6
COSMIC (genes):COQ6 COQ6
CTD Gene:51004 COQ6
dbSNP Gene:51004 COQ6
ENSEMBL:ENSG00000119723 COQ6
ENSEMBL:ENSG00000119723.17 COQ6
HGNC:20233 COQ6
KEGG Gene (Homo sapiens):51004 COQ6
Monarch:51004 COQ6
NCBI Gene:51004 COQ6
OMIM:614647 COQ6
UCSC:Q9Y2Z9 COQ6
Reference Transcript
RefSeq:NM_182476.2 COQ6
RefSeq:NM_182480.2 COQ6
Other Identifiers
11718207_a_at
11748148_a_at
11748550_a_at
16786367
218760_PM_at
218760_at
3543936
3543937
3543938
3543939
3543941
3543942
3543944
3543946
3543950
3543953
3543955
3543956
3543958
3543960
3543962
3543965
3543967
3543968
51004
56535_at
7975661
A_14_P111689
A_23_P65584
GE61232
GO:0003824
GO:0004497
GO:0005515
GO:0005739
GO:0005743
GO:0005794
GO:0006744
GO:0008681
GO:0016020
GO:0016491
GO:0016705
GO:0016709
GO:0016712
GO:0031314
GO:0042995
GO:0043226
GO:0050660
GO:0071949
GO:0106364
GO:0110142
HMNXSV003036665
ILMN_1664367
ILMN_1671356
ILMN_1783985
PH_hs_0023480
g7705593_3p_at
Participates
as a component of
COQ6:FAD [mitochondrial inner membrane] (Homo sapiens)
Cross References
RefSeq
NP_872282.1
,
NP_872286.2
OpenTargets
ENSG00000119723
HPA
ENSG00000119723-COQ6
GeneCards
Q9Y2Z9
Ensembl
ENSG00000119723
,
ENST00000334571
,
ENSP00000333946
,
ENST00000394026
,
ENSP00000377594
PRO
Q9Y2Z9
Pharos - Targets
Q9Y2Z9
Orphanet
20471
HMDB Protein
HMDBP07420
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q5HYK3 COQ5
1
COQ5 [mitochondrial matrix]
(R-HSA-2162210)
0.525
9
UniProt:Q9NZJ6 COQ3
1
COQ3(?-369) [mitochondrial matrix]
(R-HSA-2162206)
0.525
4
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