Mitochondrial COQ3 is an O-methyltransferase required in the reaction to convert 3-demethylubiquinol-10 (DeMQ10H2) to ubiquinol-10 (Q10H2) (Jonassen & Clarke 2000).
Jonassen, T, Clarke, CF
3-demethylubiquinol-10 3-O-methyltransferase activity of COQ3(?-369) [mitochondrial matrix]
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