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XylS-AGRN(30-2068) [Golgi lumen]
Stable Identifier
R-HSA-2064220
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
Golgi lumen
Synonyms
XylS-AGRN, xylosyl-AGRN, Agrin, AGRIN_HUMAN
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with glycosaminoglycan metabolism (Homo sapiens)
Defective B4GALT7 causes EDS, progeroid type (Homo sapiens)
Defective B4GALT7 does not transfer Gal to xylosyl-unit of the tetrasaccharide linker (Homo sapiens)
xylosyl-core proteins [Golgi lumen] (Homo sapiens)
XylS-AGRN(30-2068) [Golgi lumen] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of carbohydrates and carbohydrate derivatives (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Glycosaminoglycan-protein linkage region biosynthesis (Homo sapiens)
B4GALT7 transfers Gal group to xylosyl-unit of the tetrasaccharide linker (Homo sapiens)
xylosyl-core proteins [Golgi lumen] (Homo sapiens)
XylS-AGRN(30-2068) [Golgi lumen] (Homo sapiens)
XYLTs transfer Xyl to core protein (Homo sapiens)
xylosyl-core proteins [Golgi lumen] (Homo sapiens)
XylS-AGRN(30-2068) [Golgi lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:O00468 AGRN
Gene Names
AGRN, AGRIN
Chain
signal peptide:1-29, chain:30-2068, chain:30-1102, chain:1103-2068, chain:1103-1863, chain:1864-2068
Reference Genes
COSMIC (genes):AGRN AGRN
dbSNP Gene:375790 AGRN
ENSEMBL:ENSG00000188157 AGRN
Participates
as a member of
xylosyl-core proteins [Golgi lumen] (Homo sapiens)
Other forms of this molecule
HS(4)-AGRN [plasma membrane]
HS(6)-AGRN [plasma membrane]
HS(2)-AGRN [plasma membrane]
HS(1)-AGRN [plasma membrane]
HS(3)-AGRN [plasma membrane]
HS(5)-AGRN [plasma membrane]
AGRN(30-2068) [extracellular region]
GlcA-Gal-Gal-Xyl-AGRN [Golgi lumen]
GlcA-Gal-Gal-XylP-AGRN [Golgi lumen]
Gal-Gal-Xyl-AGRN [Golgi lumen]
Gal-Xyl-AGRN [Golgi lumen]
AGRN(30-2068) [Golgi lumen]
HS(2)-AGRN [Golgi lumen]
HS(3)-AGRN [Golgi lumen]
HS(1)-AGRN [Golgi lumen]
Heparan(4)-AGRN [Golgi lumen]
Heparan(3)-AGRN [Golgi lumen]
Heparan(2)-AGRN [Golgi lumen]
Heparan(1)-AGRN [Golgi lumen]
Heparan-AGRN [Golgi lumen]
HS(5)-AGRN [Golgi lumen]
HS(6)-AGRN [Golgi lumen]
HS(4)-AGRN [Golgi lumen]
HS(6)-AGRN [lysosomal lumen]
Inferred To
SP2353 [Golgi lumen]
(Drosophila melanogaster)
itx-1 [Golgi lumen]
(Caenorhabditis elegans)
AGRN [Golgi lumen]
(Bos taurus)
AGRN [Golgi lumen]
(Canis familiaris)
AGRN [Golgi lumen]
(Sus scrofa)
Homologues of XylS-AGRN(30-2068) [Golgi lumen]
(Caenorhabditis elegans)
XylS-AGRN(30-2068) [Golgi lumen]
(Caenorhabditis elegans)
XylS-AGRN(30-2068) [Golgi lumen]
(Mus musculus)
XylS-AGRN(30-2068) [Golgi lumen]
(Rattus norvegicus)
Modified Residues
Name
O-xylosyl-L-serine at unknown position
PsiMod Name
O-xylosyl-L-serine
PsiMod Definition
A protein modification that effectively converts an L-serine residue to O3-xylosylserine.
Interactors (7)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P02741 CRP
1
CRP(19-224) [extracellular region]
(R-HSA-976719)
0.643
4
UniProt:Q13438 OS9
1
OS9 [endoplasmic reticulum membrane]
(R-HSA-1022132)
0.527
3
UniProt:Q8NCB2 CAMKV
0.527
3
UniProt:O15530 PDPK1
3
p-S241-PDPK1 [cytosol]
(R-HSA-9860799)
PDPK1 [cytosol]
(R-HSA-202210)
PDPK1 [plasma membrane]
(R-HSA-61459)
0.527
2
UniProt:Q9UK22 FBXO2
1
FBXO2 [cytosol]
(R-HSA-976044)
0.527
3
UniProt:P40939 HADHA
1
HADHA [mitochondrial inner membrane]
(R-HSA-77264)
0.527
2
UniProt:O15265 ATXN7
2
ATXN7 [cytosol]
(R-HSA-201591)
ATXN7 [nucleoplasm]
(R-HSA-8869458)
0.508
2
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