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GalHyl-COL4A5
Stable Identifier
R-HSA-2023545
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
endoplasmic reticulum lumen
Synonyms
5-Gal-Hyl collagen alpha-5(IV) propeptide
Locations in the PathwayBrowser
Expand all
Extracellular matrix organization (Homo sapiens)
Collagen formation (Homo sapiens)
Collagen biosynthesis and modifying enzymes (Homo sapiens)
COLGALT1,COLGALT2:Galactosyl-hydroxylysyl collagen propeptides dissociates (Homo sapiens)
COLGALT1,COLGALT2:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Collagen chain trimerization (Homo sapiens)
Association of procollagen type IV (Homo sapiens)
Alpha-5(IV) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
C-linked procollagen type IV trimers [endoplasmic reticulum lumen] (Homo sapiens)
C-linked procollagen alpha-3(IV), alpha-4(IV) alpha-5(IV) trimer [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-5(IV) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
C-linked procollagen alpha-5(IV)X2 alpha-6(IV) trimer [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-5(IV) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Galactosylation of collagen propeptide hydroxylysines by PLOD3 (Homo sapiens)
PLOD3:Fe2+ dimer:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum membrane] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Galactosylation of collagen propeptide hydroxylysines by procollagen galactosyltransferases 1, 2. (Homo sapiens)
COLGALT1,COLGALT2:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Glucosylation of collagen propeptide hydroxylysines (Homo sapiens)
PLOD3:Fe2+ dimer:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum membrane] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
PLOD3:Fe2+ dimer:Galactosyl-hydroxylysyl collagen propeptides dissociates (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
PLOD3:Fe2+ dimer:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum membrane] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Procollagen triple helix formation (Homo sapiens)
Collagen and procollagen triple helices:Serpin H1 [endoplasmic reticulum lumen] (Homo sapiens)
Collagen and procollagen triple helices [endoplasmic reticulum lumen] (Homo sapiens)
Non-fibrillar collagens [endoplasmic reticulum lumen] (Homo sapiens)
Tropocollagen type IV [endoplasmic reticulum lumen] (Homo sapiens)
Tropocollagen alpha-3(IV), alpha-4(IV), alpha-5(IV) [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-5(IV) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Tropocollagen alpha-5(IV)X2 alpha-6(IV) [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-5(IV) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Procollagen C-linked trimers [endoplasmic reticulum lumen] (Homo sapiens)
C-linked procollagen type IV trimers [endoplasmic reticulum lumen] (Homo sapiens)
C-linked procollagen alpha-3(IV), alpha-4(IV) alpha-5(IV) trimer [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-5(IV) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
C-linked procollagen alpha-5(IV)X2 alpha-6(IV) trimer [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-5(IV) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Secretion of collagens (Homo sapiens)
Collagens and tropocollagens:Serpin H1 [endoplasmic reticulum lumen] (Homo sapiens)
Collagens and tropocollagens [endoplasmic reticulum lumen] (Homo sapiens)
Non-fibrillar collagens [endoplasmic reticulum lumen] (Homo sapiens)
Tropocollagen type IV [endoplasmic reticulum lumen] (Homo sapiens)
Tropocollagen alpha-3(IV), alpha-4(IV), alpha-5(IV) [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-5(IV) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
Tropocollagen alpha-5(IV)X2 alpha-6(IV) [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-5(IV) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:P29400 COL4A5
Gene Names
COL4A5
Chain
signal peptide:1-26, chain:27-1685
Reference Genes
BioGPS Gene:1287 COL4A5
COSMIC (genes):COL4A5 COL4A5
CTD Gene:1287 COL4A5
dbSNP Gene:1287 COL4A5
ENSEMBL:ENSG00000188153 COL4A5
HGNC:2207 COL4A5
KEGG Gene (Homo sapiens):hsa:1287 COL4A5
Monarch:1287 COL4A5
NCBI Gene:1287 COL4A5
OMIM:303630 COL4A5
UCSC:P29400 COL4A5
Reference Transcript
RefSeq:NM_033380.2 COL4A5
RefSeq:NM_000495.4 COL4A5
Other Identifiers
0005890047
11724094_a_at
11757903_s_at
1287
17106102
213110_s_at
234387_at
32667_at
65449
8169294
A_23_P45365
A_24_P290153
AAA51558
AAA52045
AAA52046
AAA99480
AAB33374
AAC27816
AAC60612
AAD13909
AAF66217
AF199451
AF199452
AL031622
AL034369
AL035425
AL136364
CAA22267
CAA85512
CAB90289
CAI43038
CCDS14543
CCDS35366
CH471120
COL4A5
COL4A5-201
COL4A5-202
EAX02683
ENSG00000188153
ENSP00000331902
ENSP00000354505
ENST00000328300
ENST00000361603
EntrezGene:1287
GE58224
GO:0003674
GO:0005198
GO:0005201
GO:0005575
GO:0005576
GO:0005578
GO:0005581
GO:0005587
GO:0005604
GO:0005605
GO:0005622
GO:0005623
GO:0005737
GO:0005783
GO:0005788
GO:0007165
GO:0007528
GO:0008150
GO:0009056
GO:0030198
GO:0030574
GO:0031594
GO:0038063
GO:0043226
GO:0043234
HGNC:2207
HPA065449
Hs.169825.0.A2_3p_a_at
Hs.279021.0.S1_3p_at
Hs.369089
ILMN_1742534
ILMN_2375360
IPR001442
IPR008160
IPR016187
M31115
M58526
M63455
M63456
M63457
M63458
M63459
M63460
M63461
M63462
M63463
M63464
M63465
M63466
M63467
M63468
M63470
M63471
M63472
M63473
M90464
MIM:301050
MIM:303630
NM_000495
NM_033380
NP_000486
NP_203699
PF01391
PF01413
PH_hs_0010122
S59334
S69168
S75903
SM00111
TC0X000532.hg
TC0X001822.hg
U04470
U04471
U04472
U04473
U04474
U04476
U04477
U04478
U04479
U04480
U04483
U04485
U04486
U04487
U04488
U04489
U04490
U04491
U04492
U04493
U04494
U04495
U04496
U04497
U04498
U04499
U04500
U04501
U04502
U04503
U04504
U04505
U04506
U04507
U04508
U04509
U04510
U04511
U04512
U04514
U04515
U04516
U04517
U04518
U04519
U04520
uc004enz.3
uc065aqj.1
UPI000002A538
UPI0000126D57
XM_011530849
XM_017029259
XM_017029260
XM_017029261
XM_017029262
XM_017029263
XP_011529151
XP_016884748
XP_016884749
XP_016884750
XP_016884751
XP_016884752
Z37153
Participant Of
hasMember
Alpha-5(IV) chains [endoplasmic reticulum lumen]
hasCandidate
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen]
Other forms of this molecule
3x4Hyp-3Hyp-GlcGalHyl-COL4A5 [endoplasmic reticulum lumen]
GlcGalHyl-COL4A5 [endoplasmic reticulum lumen]
3x4Hyp-GlcGalHyl-COL4A5 [endoplasmic reticulum lumen]
3x4Hyp-3Hyp-GalHyl-COL4A5 [endoplasmic reticulum lumen]
3x4Hyp-GalHyl-COL4A5 [endoplasmic reticulum lumen]
COL4A5 [endoplasmic reticulum lumen]
3x4Hyp-COL4A5 [endoplasmic reticulum lumen]
3x4Hyp-3Hyp-COL4A5 [endoplasmic reticulum lumen]
3x4Hyp-5Hyl-COL4A5 [endoplasmic reticulum lumen]
3x4Hyp-3Hyp-5Hyl-COL4A5 [endoplasmic reticulum lumen]
5Hyl-COL4A5 [endoplasmic reticulum lumen]
3,4-Hyp 5-sulfiliminyl collagen alpha-5(IV) chain [extracellular region]
5-sulfiliminyl collagen alpha-5(IV) chain [extracellular region]
4-Hyp 5-sulfiliminyl collagen alpha-5(IV) chain [extracellular region]
GlcGalHyl-COL4A5(27-?) [extracellular region]
3x4Hyp-5Hyl-COL4A5(?-1685) [extracellular region]
3x4Hyp-GlcGalHyl-COL4A5(?-1685) [extracellular region]
COL4A5(?-1685) [extracellular region]
3x4Hyp-COL4A5(27-?) [extracellular region]
3x4Hyp-3Hyp-GalHyl-COL4A5(27-?) [extracellular region]
3x4Hyp-3Hyp-GlcGalHyl-COL4A5(?-1685) [extracellular region]
3x4Hyp-3Hyp-GlcGalHyl-COL4A5(27-?) [extracellular region]
GalHyl-COL4A5(27-?) [extracellular region]
3x4Hyp-3Hyp-5Hyl-COL4A5(27-?) [extracellular region]
3x4Hyp-GalHyl-COL4A5(27-?) [extracellular region]
COL4A5(27-?) [extracellular region]
3x4Hyp-3Hyp-COL4A5(?-1685) [extracellular region]
3x4Hyp-GalHyl-COL4A5 [extracellular region]
3x4Hyp-3Hyp-COL4A5 [extracellular region]
3x4Hyp-GlcGalHyl-COL4A5 [extracellular region]
3x4Hyp-3Hyp-5Hyl-COL4A5 [extracellular region]
5Hyl-COL4A5 [extracellular region]
3x4Hyp-5Hyl-COL4A5 [extracellular region]
3x4Hyp-COL4A5 [extracellular region]
GlcGalHyl-COL4A5 [extracellular region]
3x4Hyp-3Hyp-GalHyl-COL4A5 [extracellular region]
3x4Hyp-3Hyp-GlcGalHyl-COL4A5 [extracellular region]
COL4A5 [extracellular region]
GalHyl-COL4A5 [extracellular region]
COL4A5(27-?) [extracellular region]
5Hyl-COL4A5(27-?) [extracellular region]
3x4Hyp-3Hyp-GalHyl-COL4A5(?-1685) [extracellular region]
3x4Hyp-GalHyl-COL4A5(?-1685) [extracellular region]
3x4Hyp-5Hyl-COL4A5(27-?) [extracellular region]
GlcGalHyl-COL4A5(?-1685) [extracellular region]
3x4Hyp-3Hyp-COL4A5(27-?) [extracellular region]
3x4Hyp-3Hyp-5Hyl-COL4A5(?-1685) [extracellular region]
5Hyl-COL4A5(?-1685) [extracellular region]
3x4Hyp-GlcGalHyl-COL4A5(27-?) [extracellular region]
3x4Hyp-COL4A5(?-1685) [extracellular region]
GalHyl-COL4A5(?-1685) [extracellular region]
Inferred To
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Bos taurus)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Canis familiaris)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Danio rerio)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Gallus gallus)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Mus musculus)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Rattus norvegicus)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Sus scrofa)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Taeniopygia guttata)
GalHyl-COL4A5 [endoplasmic reticulum lumen] (Xenopus tropicalis)
Homologues of GalHyl-COL4A5 [endoplasmic reticulum lumen] (Canis familiaris)
Homologues of GalHyl-COL4A5 [endoplasmic reticulum lumen] (Danio rerio)
Homologues of GalHyl-COL4A5 [endoplasmic reticulum lumen] (Mus musculus)
Homologues of GalHyl-COL4A5 [endoplasmic reticulum lumen] (Taeniopygia guttata)
Modified Residues
Name
O5-galactosyl-L-hydroxylysine at unknown position
PsiMod Name
O5-galactosyl-L-hydroxylysine
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to O5-galactosyl-L-hydroxylysine.
Cross References
RefSeq
NP_203699.1
,
NP_000486.1
GeneCards
P29400
PRO
P29400
Orphanet
15774
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