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GalHyl-COL7A1 [endoplasmic reticulum lumen]
Stable Identifier
R-HSA-2023540
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
endoplasmic reticulum lumen
Synonyms
5-Gal-Hyl collagen alpha-1(VII) chain, COL7A1, CO7A1_HUMAN
Locations in the PathwayBrowser
Expand all
Extracellular matrix organization (Homo sapiens)
Collagen formation (Homo sapiens)
Collagen biosynthesis and modifying enzymes (Homo sapiens)
COLGALT1,COLGALT2:Galactosyl-hydroxylysyl collagen propeptides dissociates (Homo sapiens)
COLGALT1,COLGALT2:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Collagen chain trimerization (Homo sapiens)
Association of procollagen type VII (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
C-linked procollagen type VII trimer [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Galactosylation of collagen propeptide hydroxylysines by PLOD3 (Homo sapiens)
PLOD3:Fe2+ dimer:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum membrane] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Galactosylation of collagen propeptide hydroxylysines by procollagen galactosyltransferases 1, 2. (Homo sapiens)
COLGALT1,COLGALT2:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Glucosylation of collagen propeptide hydroxylysines (Homo sapiens)
PLOD3:Fe2+ dimer:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum membrane] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
PLOD3:Fe2+ dimer:Galactosyl-hydroxylysyl collagen propeptides dissociates (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
PLOD3:Fe2+ dimer:Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum membrane] (Homo sapiens)
Galactosyl-hydroxylysyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Procollagen triple helix formation (Homo sapiens)
Collagen and procollagen triple helices:Serpin H1 [endoplasmic reticulum lumen] (Homo sapiens)
Collagen and procollagen triple helices [endoplasmic reticulum lumen] (Homo sapiens)
Non-fibrillar collagens [endoplasmic reticulum lumen] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Procollagen C-linked trimers [endoplasmic reticulum lumen] (Homo sapiens)
C-linked procollagen type VII trimer [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Secretion of collagens (Homo sapiens)
Collagens and tropocollagens:Serpin H1 [endoplasmic reticulum lumen] (Homo sapiens)
Collagens and tropocollagens [endoplasmic reticulum lumen] (Homo sapiens)
Non-fibrillar collagens [endoplasmic reticulum lumen] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Asparagine N-linked glycosylation (Homo sapiens)
Transport to the Golgi and subsequent modification (Homo sapiens)
ER to Golgi Anterograde Transport (Homo sapiens)
COPII-mediated vesicle transport (Homo sapiens)
Inner coat assembly and cargo binding (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Loss of SAR1B GTPase (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
SEC16 complex binds SAR1B:GTP:SEC23:SEC24 (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
SEC31:SEC13 and v-SNARE recruitment (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer:SEC13:SEC31:SEC23IP:v-SNARES [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Vesicle budding (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer:SEC13:SEC31:SEC23IP:v-SNARES [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Cargo concentration in the ER (Homo sapiens)
CTAGE5 and MIA3 dissociate from procollagen VII vesicle (Homo sapiens)
procollagen VII:MIA3:CTAGE5:PREB:SEC23A:SEC24C [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII:MIA3 [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
CTAGE5 and MIA3 load procollagen VII into COPII vesicles (Homo sapiens)
Procollagen type VII:MIA3 [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
procollagen VII:MIA3:CTAGE5:PREB:SEC23A:SEC24C [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII:MIA3 [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Inner coat assembly and cargo binding (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
MIA3 binds procollagen VII (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Procollagen type VII:MIA3 [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Vesicle-mediated transport (Homo sapiens)
Membrane Trafficking (Homo sapiens)
ER to Golgi Anterograde Transport (Homo sapiens)
COPII-mediated vesicle transport (Homo sapiens)
Inner coat assembly and cargo binding (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Loss of SAR1B GTPase (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
SEC16 complex binds SAR1B:GTP:SEC23:SEC24 (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
SEC31:SEC13 and v-SNARE recruitment (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer:SEC13:SEC31:SEC23IP:v-SNARES [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Vesicle budding (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer:SEC13:SEC31:SEC23IP:v-SNARES [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Cargo concentration in the ER (Homo sapiens)
CTAGE5 and MIA3 dissociate from procollagen VII vesicle (Homo sapiens)
procollagen VII:MIA3:CTAGE5:PREB:SEC23A:SEC24C [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII:MIA3 [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
CTAGE5 and MIA3 load procollagen VII into COPII vesicles (Homo sapiens)
Procollagen type VII:MIA3 [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
procollagen VII:MIA3:CTAGE5:PREB:SEC23A:SEC24C [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII:MIA3 [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Inner coat assembly and cargo binding (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
procollagen VII:SEC24C:SEC23A [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
MIA3 binds procollagen VII (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
Procollagen type VII:MIA3 [endoplasmic reticulum membrane] (Homo sapiens)
Procollagen type VII [endoplasmic reticulum lumen] (Homo sapiens)
Alpha-1(VII) chains [endoplasmic reticulum lumen] (Homo sapiens)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q02388 COL7A1
Gene Names
COL7A1
Chain
signal peptide:1-16, chain:17-2944
Reference Genes
BioGPS Gene:1294 COL7A1
COSMIC (genes):COL7A1 COL7A1
CTD Gene:1294 COL7A1
dbSNP Gene:1294 COL7A1
ENSEMBL:ENSG00000114270 COL7A1
ENSEMBL_homo_sapiens_GENE:ENSG00000114270 COL7A1
HGNC:2214 COL7A1
KEGG Gene (Homo sapiens):1294 COL7A1
Monarch:1294 COL7A1
NCBI Gene:1294 COL7A1
OMIM:120120 COL7A1
UCSC:Q02388 COL7A1
Reference Transcript
RefSeq:XM_011533337.1 COL7A1
RefSeq:NM_000094.3 COL7A1
Other Identifiers
0005130047
11721705_at
1294
16357
16953458
204136_at
217312_s_at
2673347
2673348
2673350
2673353
2673354
2673356
2673357
2673359
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2673385
2673388
2673389
2673392
2673394
2673396
2673397
2673399
2673400
2673401
2673402
2673403
2673404
2673405
2673406
2673407
2673408
2673409
2673411
2673414
2673416
2673417
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2673424
2673425
2673426
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2673453
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2673456
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2673475
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2673487
2673489
2673490
2673492
2673493
2673494
2673495
2673496
2673497
2673498
2673499
2673500
32123_at
42420
8086985
AAA36357
AAA58965
AAA75438
AAA89196
AAA96439
AAB24637
BAA02853
C9JBL3
CAB016357
CCDS2773
COL7A1
COL7A1-201
D13694
ENSG00000114270
ENSP00000332371
ENST00000328333
EntrezGene:1294
g4502960_3p_at
GE57549
GO:0000139
GO:0000902
GO:0003429
GO:0003674
GO:0004867
GO:0005198
GO:0005515
GO:0005575
GO:0005576
GO:0005581
GO:0005590
GO:0005604
GO:0005615
GO:0005622
GO:0005623
GO:0005737
GO:0005783
GO:0005788
GO:0005794
GO:0006810
GO:0006888
GO:0007155
GO:0008150
GO:0008544
GO:0009790
GO:0010466
GO:0010951
GO:0016192
GO:0022607
GO:0030020
GO:0030134
GO:0030154
GO:0030198
GO:0030234
GO:0030414
GO:0031012
GO:0031410
GO:0032991
GO:0033116
GO:0035987
GO:0040007
GO:0043226
GO:0048208
GO:0048646
GO:0048856
GO:0061024
GO:0062023
GO:0065003
HGNC:2214
HPA042420
Hs.1640.1.S1_3p_a_at
ILMN_1751161
IPR002035
IPR002223
IPR003961
IPR008160
IPR013783
IPR020901
IPR036116
IPR036465
IPR036880
L02870
L06862
L23982
LRG_286
M65158
M96984
MIM:120120
MIM:131705
MIM:131750
MIM:131850
MIM:132000
MIM:226600
MIM:604129
MIM:607523
NM_000094
NP_000085
PF00014
PF00041
PF00092
PF01391
PH_hs_0000224
PR00453
PR00759
S51236
SM00060
SM00327
TC03001382.hg
uc003ctz.3
UPI0000126D20
XM_011533337
XM_017005688
XM_017005689
XM_017005690
XM_017005691
XM_017005692
XP_011531639
XP_016861177
XP_016861178
XP_016861179
XP_016861180
XP_016861181
XR_001740003
XR_001740004
XR_001740005
XR_001740006
XR_001740007
XR_001740008
Participant Of
hasCandidate
5-Gal-Hyl collagen propeptides [endoplasmic reticulum lumen]
hasMember
Alpha-1(VII) chains [endoplasmic reticulum lumen]
Other forms of this molecule
3x4Hyp-3Hyp-5Hyl-COL7A1(2822-2944) [extracellular region]
5Hyl-COL7A1(2822-2944) [extracellular region]
3x4Hyp-3Hyp-COL7A1(2822-2944) [extracellular region]
3x4Hyp-5Hyl-COL7A1(2822-2944) [extracellular region]
3x4Hyp-3Hyp-GalHyl-COL7A1(2822-2944) [extracellular region]
COL7A1(2822-2944) [extracellular region]
3x4Hyp-GlcGalHyl-COL7A1(2822-2944) [extracellular region]
3x4Hyp-GalHyl-COL7A1(2822-2944) [extracellular region]
3x4Hyp-COL7A1(2822-2944) [extracellular region]
3x4Hyp-3Hyp-GlcGalHyl-COL7A1(2822-2944) [extracellular region]
GlcGalHyl-COL7A1(2822-2944) [extracellular region]
GalHyl-COL7A1(2822-2944) [extracellular region]
COL7A1 [extracellular region]
3x4Hyp-3Hyp-GlcGalHyl-COL7A1 [extracellular region]
GalHyl-COL7A1 [extracellular region]
3x4Hyp-3Hyp-COL7A1 [extracellular region]
3x4Hyp-COL7A1 [extracellular region]
3x4Hyp-5Hyl-COL7A1 [extracellular region]
GlcGalHyl-COL7A1 [extracellular region]
3x4Hyp-3Hyp-5Hyl-COL7A1 [extracellular region]
3x4Hyp-GlcGalHyl-COL7A1 [extracellular region]
3x4Hyp-3Hyp-GalHyl-COL7A1 [extracellular region]
5Hyl-COL7A1 [extracellular region]
3x4Hyp-GalHyl-COL7A1 [extracellular region]
3x4Hyp-GalHyl-COL7A1(?-2944) [extracellular region]
3x4Hyp-GlcGalHyl-COL7A1(17-?) [extracellular region]
3x4Hyp-3Hyp-COL7A1(?-2944) [extracellular region]
3x4Hyp-COL7A1(?-2944) [extracellular region]
GlcGalHyl-COL7A1(17-?) [extracellular region]
3x4Hyp-5Hyl-COL7A1(?-2944) [extracellular region]
3x4Hyp-3Hyp-5Hyl-COL7A1(?-2944) [extracellular region]
3x4Hyp-3Hyp-GalHyl-COL7A1(17-?) [extracellular region]
GalHyl-COL7A1(?-2944) [extracellular region]
3x4Hyp-3Hyp-GalHyl-COL7A1(?-2944) [extracellular region]
COL7A1(17-?) [extracellular region]
3x4Hyp-3Hyp-GlcGalHyl-COL7A1(?-2944) [extracellular region]
3x4Hyp-3Hyp-GlcGalHyl-COL7A1(17-?) [extracellular region]
COL7A1(?-2944) [extracellular region]
3x4Hyp-COL7A1(17-?) [extracellular region]
3x4Hyp-3Hyp-COL7A1(17-?) [extracellular region]
GalHyl-COL7A1(17-?) [extracellular region]
GlcGalHyl-COL7A1(?-2944) [extracellular region]
3x4Hyp-3Hyp-5Hyl-COL7A1(17-?) [extracellular region]
3x4Hyp-5Hyl-COL7A1(17-?) [extracellular region]
3x4Hyp-GalHyl-COL7A1(17-?) [extracellular region]
3x4Hyp-GlcGalHyl-COL7A1(?-2944) [extracellular region]
5Hyl-COL7A1(?-2944) [extracellular region]
5Hyl-COL7A1(17-?) [extracellular region]
5Hyl-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
3x4Hyp-5Hyl-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
3x4Hyp-3Hyp-5Hyl-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
GalHyl-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
GlcGalHyl-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
3x4Hyp-3Hyp-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
3x4Hyp-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
3x4Hyp-GalHyl-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
3x4Hyp-3Hyp-GalHyl-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
3x4Hyp-GlcGalHyl-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
3x4Hyp-3Hyp-GlcGalHyl-COL7A1 [endoplasmic reticulum-Golgi intermediate compartment membrane]
5Hyl-COL7A1 [COPII-coated ER to Golgi transport vesicle]
3x4Hyp-5Hyl-COL7A1 [COPII-coated ER to Golgi transport vesicle]
GlcGalHyl-COL7A1 [COPII-coated ER to Golgi transport vesicle]
COL7A1 [COPII-coated ER to Golgi transport vesicle]
3x4Hyp-COL7A1 [COPII-coated ER to Golgi transport vesicle]
3x4Hyp-3Hyp-COL7A1 [COPII-coated ER to Golgi transport vesicle]
3x4Hyp-GalHyl-COL7A1 [COPII-coated ER to Golgi transport vesicle]
3x4Hyp-3Hyp-GalHyl-COL7A1 [COPII-coated ER to Golgi transport vesicle]
GalHyl-COL7A1 [COPII-coated ER to Golgi transport vesicle]
3x4Hyp-GlcGalHyl-COL7A1 [COPII-coated ER to Golgi transport vesicle]
3x4Hyp-3Hyp-GlcGalHyl-COL7A1 [COPII-coated ER to Golgi transport vesicle]
3x4Hyp-3Hyp-5Hyl-COL7A1 [COPII-coated ER to Golgi transport vesicle]
3x4Hyp-GlcGalHyl-COL7A1 [endoplasmic reticulum lumen]
3x4Hyp-GalHyl-COL7A1 [endoplasmic reticulum lumen]
3x4Hyp-GalHyl-COL7A1(17-2821) [extracellular region]
GalHyl-COL7A1(17-2821) [extracellular region]
3x4Hyp-3Hyp-COL7A1(17-2821) [extracellular region]
5Hyl-COL7A1(17-2821) [extracellular region]
3x4Hyp-3Hyp-GlcGalHyl-COL7A1(17-2821) [extracellular region]
COL7A1(17-2821) [extracellular region]
3x4Hyp-5Hyl-COL7A1(17-2821) [extracellular region]
3x4Hyp-3Hyp-GalHyl-COL7A1(17-2821) [extracellular region]
3x4Hyp-GlcGalHyl-COL7A1(17-2821) [extracellular region]
3x4Hyp-COL7A1(17-2821) [extracellular region]
GlcGalHyl-COL7A1(17-2821) [extracellular region]
3x4Hyp-3Hyp-5Hyl-COL7A1(17-2821) [extracellular region]
3x4Hyp-3Hyp-COL7A1 [endoplasmic reticulum lumen]
3x4Hyp-3Hyp-GalHyl-COL7A1 [endoplasmic reticulum lumen]
5Hyl-COL7A1 [endoplasmic reticulum lumen]
COL7A1 [endoplasmic reticulum lumen]
GlcGalHyl-COL7A1 [endoplasmic reticulum lumen]
3x4Hyp-3Hyp-5Hyl-COL7A1 [endoplasmic reticulum lumen]
3x4Hyp-3Hyp-GlcGalHyl-COL7A1 [endoplasmic reticulum lumen]
3x4Hyp-COL7A1 [endoplasmic reticulum lumen]
3x4Hyp-5Hyl-COL7A1 [endoplasmic reticulum lumen]
Inferred To
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Bos taurus)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Canis familiaris)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Danio rerio)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Gallus gallus)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Mus musculus)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Rattus norvegicus)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Sus scrofa)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Taeniopygia guttata)
GalHyl-COL7A1 [endoplasmic reticulum lumen] (Xenopus tropicalis)
Homologues of GalHyl-COL7A1 [endoplasmic reticulum lumen] (Danio rerio)
Modified Residues
Name
O5-galactosyl-L-hydroxylysine at unknown position
PsiMod Name
O5-galactosyl-L-hydroxylysine
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to O5-galactosyl-L-hydroxylysine.
Cross References
RefSeq
XP_011531639.1
,
NP_000085.1
OpenTargets
ENSG00000114270
GeneCards
Q02388
PRO
Q02388
Orphanet
15781
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q5JRA6 MIA3
3
MIA3 [endoplasmic reticulum lumen]
(R-HSA-8956743)
p-MIA3 [endoplasmic reticulum lumen]
(R-HSA-8957064)
MIA3 [endoplasmic reticulum membrane]
(R-HSA-5689472)
0.524
2
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