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ACOX2 [peroxisomal matrix]
Stable Identifier
R-HSA-192321
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
peroxisomal matrix
Synonyms
Acyl-coenzyme A oxidase 2, peroxisomal
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Peroxisomal lipid metabolism (Homo sapiens)
Beta-oxidation of pristanoyl-CoA (Homo sapiens)
ACOX2:FAD, ACOXL:FAD oxidise (2S)-pristanoyl-CoA to trans-2,3-dehydropristanoyl-CoA (Homo sapiens)
ACOX2:FAD, ACOXL:FAD [peroxisomal matrix] (Homo sapiens)
ACOX2:FAD [peroxisomal matrix] (Homo sapiens)
ACOX2 [peroxisomal matrix] (Homo sapiens)
Metabolism of steroids (Homo sapiens)
Bile acid and bile salt metabolism (Homo sapiens)
Synthesis of bile acids and bile salts (Homo sapiens)
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Homo sapiens)
25(S) DHCA-CoA is dehydrogenated to 25(S) 3alpha,7alpha-dihydroxy-5beta-cholest-24-enoyl-CoA (Homo sapiens)
ACOX2:FAD [peroxisomal matrix] (Homo sapiens)
ACOX2 [peroxisomal matrix] (Homo sapiens)
25(S) THCA-CoA is dehydrogenated to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholest-24-enoyl-CoA (THCA-CoA) (Homo sapiens)
ACOX2:FAD [peroxisomal matrix] (Homo sapiens)
ACOX2 [peroxisomal matrix] (Homo sapiens)
Protein localization (Homo sapiens)
Peroxisomal protein import (Homo sapiens)
Cargo of PEX5S,L translocates from the cytosol to the peroxisomal matrix (Homo sapiens)
Cargo proteins containing PTS1 [peroxisomal matrix] (Homo sapiens)
ACOX2 [peroxisomal matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q99424 ACOX2
Gene Names
ACOX2
Chain
chain:1-681
Reference Genes
BioGPS Gene:8309 ACOX2
COSMIC (genes):ACOX2 ACOX2
CTD Gene:8309 ACOX2
dbSNP Gene:8309 ACOX2
ENSEMBL:ENSG00000168306 ACOX2
ENSEMBL_homo_sapiens_GENE:ENSG00000168306.13 ACOX2
HGNC:120 ACOX2
Monarch:8309 ACOX2
NCBI Gene:8309 ACOX2
OMIM:601641 ACOX2
UCSC:Q99424 ACOX2
Reference Transcript
RefSeq:NM_003500.3 ACOX2
RefSeq:XM_005265505.1 ACOX2
Other Identifiers
11721223_at
16955535
205364_PM_at
205364_at
2678403
2678404
2678407
2678410
2678413
2678414
2678419
2678420
2678423
2678428
2678430
2678432
2678434
2678436
2678437
2678438
2678442
2678443
2678446
38348_at
8088397
8309
A_23_P10182
GE60170
GO:0000038
GO:0003824
GO:0003997
GO:0005504
GO:0005515
GO:0005777
GO:0005782
GO:0005829
GO:0006629
GO:0006631
GO:0006635
GO:0006699
GO:0008289
GO:0016401
GO:0016491
GO:0016627
GO:0033540
GO:0033791
GO:0042803
GO:0043226
GO:0043231
GO:0050660
GO:0055088
GO:0071949
TC03001500.hg
X95190_at
g4501868_3p_at
Participates
as a member of
Cargo proteins containing PTS1 [peroxisomal matrix] (Homo sapiens)
as a component of
ACOX2:FAD [peroxisomal matrix] (Homo sapiens)
Other forms of this molecule
ACOX2 [cytosol]
Inferred To
Acox2 [peroxisomal matrix]
(Mus musculus)
Acox2 [peroxisomal matrix]
(Rattus norvegicus)
Homologues of ACOX2 [peroxisomal matrix]
(Caenorhabditis elegans)
Homologues of ACOX2 [peroxisomal matrix]
(Drosophila melanogaster)
ACOX2 [peroxisomal matrix]
(Bos taurus)
ACOX2 [peroxisomal matrix]
(Caenorhabditis elegans)
ACOX2 [peroxisomal matrix]
(Canis familiaris)
ACOX2 [peroxisomal matrix]
(Dictyostelium discoideum)
ACOX2 [peroxisomal matrix]
(Drosophila melanogaster)
ACOX2 [peroxisomal matrix]
(Gallus gallus)
ACOX2 [peroxisomal matrix]
(Sus scrofa)
ACOX2 [peroxisomal matrix]
(Xenopus tropicalis)
Cross References
RefSeq
XP_005265562.1
,
NP_003491.1
OpenTargets
ENSG00000168306
IntEnz
1.17.99.3
GeneCards
Q99424
HPA
ENSG00000168306-ACOX2
Ensembl
ENST00000302819
,
ENSG00000168306
,
ENSP00000307697
PRO
Q99424
Pharos - Targets
Q99424
Orphanet
24326
HMDB Protein
HMDBP00164
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