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PPOX [mitochondrial intermembrane space]
Stable Identifier
R-HSA-189434
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial intermembrane space
Synonyms
Protoporphyrinogen oxidase, PPOX_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of porphyrins (Homo sapiens)
Heme biosynthesis (Homo sapiens)
PPO oxidises PPGEN9 to PRIN9 (Homo sapiens)
2xPPOX:FAD [mitochondrial intermembrane space] (Homo sapiens)
PPOX [mitochondrial intermembrane space] (Homo sapiens)
External Reference Information
External Reference
UniProt:P50336 PPOX
Gene Names
PPOX
Chain
chain:1-477
Reference Genes
BioGPS Gene:5498 PPOX
COSMIC (genes):PPOX PPOX
CTD Gene:5498 PPOX
dbSNP Gene:5498 PPOX
ENSEMBL:ENSG00000143224 PPOX
HGNC:9280 PPOX
KEGG:hsa:5498 PPOX
Monarch:5498 PPOX
NCBI Gene:5498 PPOX
OMIM:600923 PPOX
UCSC:P50336 PPOX
Reference Transcript
RefSeq:NM_000309.5 PPOX
RefSeq:NM_001365398.1 PPOX
RefSeq:NM_001122764.3 PPOX
Other Identifiers
11722711_a_at
11722712_x_at
11762307_a_at
16672779
204788_PM_s_at
204788_s_at
2363485
2363486
2363487
2363488
2363490
2363491
2363492
2363493
2363494
2363495
2363496
2363497
2363498
2363499
2363500
2363501
2363502
2363503
2363504
2363505
2363506
2363507
2363508
2363509
2363510
2363511
2363512
2363513
2363515
2363516
2363517
2363519
2363520
238117_PM_at
238117_at
238118_PM_s_at
238118_s_at
37098_at
5498
7906688
A_14_P111122
A_14_P121393
A_23_P201400
A_24_P102726
D38537_s_at
GE79427
GO:0003824
GO:0004729
GO:0005739
GO:0005743
GO:0005758
GO:0006779
GO:0006782
GO:0006783
GO:0006784
GO:0006785
GO:0016491
GO:0031966
GO:0043226
GO:0048034
GO:0050660
GO:0070819
HMNXSV003038664
HMNXSV003041228
Hs.157267.0.A1_3p_at
Hs.157267.0.A1_3p_x_at
ILMN_1673798
PH_hs_0018309
g4506000_3p_a_at
Participates
as a component of
2xPPOX:FAD [mitochondrial intermembrane space] (Homo sapiens)
Inferred To
HEM14 [mitochondrial intermembrane space]
(Saccharomyces cerevisiae)
Ppox [mitochondrial intermembrane space]
(Drosophila melanogaster)
Ppox [mitochondrial intermembrane space]
(Mus musculus)
Ppox [mitochondrial intermembrane space]
(Rattus norvegicus)
PPOX [mitochondrial intermembrane space]
(Bos taurus)
PPOX [mitochondrial intermembrane space]
(Canis familiaris)
PPOX [mitochondrial intermembrane space]
(Gallus gallus)
PPOX [mitochondrial intermembrane space]
(Plasmodium falciparum)
PPOX [mitochondrial intermembrane space]
(Sus scrofa)
hem14 [mitochondrial intermembrane space]
(Schizosaccharomyces pombe)
ppox [mitochondrial intermembrane space]
(Danio rerio)
ppox [mitochondrial intermembrane space]
(Dictyostelium discoideum)
ppox [mitochondrial intermembrane space]
(Xenopus tropicalis)
Cross References
RefSeq
NP_001352327.1
,
NP_001116236.1
,
NP_000300.1
ENSEMBL
ENST00000352210
,
ENSG00000143224
,
ENST00000367999
,
ENSP00000356978
,
ENSP00000343943
OpenTargets
ENSG00000143224
ZINC - Substances
PPOX_HUMAN
ZINC - Biogenic
PPOX_HUMAN
ZINC target
P50336
PRO
P50336
PDB
4IVM
,
3NKS
,
4IVO
ZINC - Metabolites
PPOX_HUMAN
GeneCards
PPOX
HPA
ENSG00000143224-PPOX
Pharos - Targets
P50336
Orphanet
PPOX
ZINC - Predictions - Purchasable
PPOX_HUMAN
HMDB Protein
HMDBP01021
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O95861 BPNT1
1
BPNT1 [cytosol]
(R-HSA-176573)
0.527
2
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