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ACSM1 [mitochondrial matrix]
Stable Identifier
R-HSA-177123
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
middle-chain acyl-CoA synthetase 1
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Biological oxidations (Homo sapiens)
Phase II - Conjugation of compounds (Homo sapiens)
Amino Acid conjugation (Homo sapiens)
Conjugation of carboxylic acids (Homo sapiens)
Conjugation of benzoate with glycine (Homo sapiens)
benzoate + Coenzyme A + ATP => benzoyl-CoA + AMP + pyrophosphate (Homo sapiens)
xenobiotic/medium-chain fatty acid:CoA ligases [mitochondrial matrix] (Homo sapiens)
ACSM1 [mitochondrial matrix] (Homo sapiens)
Conjugation of phenylacetate with glutamine (Homo sapiens)
phenylacetate + Coenzyme A + ATP => phenylacetyl-CoA + AMP + pyrophosphate (Homo sapiens)
xenobiotic/medium-chain fatty acid:CoA ligases [mitochondrial matrix] (Homo sapiens)
ACSM1 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q08AH1 ACSM1
Gene Names
ACSM1, BUCS1, LAE, MACS1
Chain
transit peptide:1-31, chain:32-577
Reference Genes
BioGPS Gene:116285 ACSM1
COSMIC (genes):ACSM1 ACSM1
CTD Gene:116285 ACSM1
dbSNP Gene:116285 ACSM1
ENSEMBL:ENSG00000166743 ACSM1
HGNC:18049 ACSM1
KEGG Gene (Homo sapiens):116285 ACSM1
Monarch:116285 ACSM1
NCBI Gene:116285 ACSM1
OMIM:614357 ACSM1
UCSC:Q08AH1 ACSM1
Reference Transcript
RefSeq:NM_001318890.1 ACSM1
RefSeq:NM_052956.2 ACSM1
Other Identifiers
0002230497
116285
11740696_a_at
16824655
215432_at
34050_at
3683741
3683742
3683744
3683745
3683746
3683747
3683748
3683749
3683750
3683754
3683756
3683757
3683758
3683760
3683762
3683763
3683764
3683765
3683768
3683769
7999981
A_23_P106933
GE83690
GO:0000166
GO:0003674
GO:0003824
GO:0003996
GO:0004321
GO:0005515
GO:0005524
GO:0005525
GO:0005575
GO:0005576
GO:0005615
GO:0005622
GO:0005737
GO:0005739
GO:0005759
GO:0006091
GO:0006629
GO:0006631
GO:0006633
GO:0006637
GO:0006790
GO:0006805
GO:0008150
GO:0009058
GO:0015645
GO:0015980
GO:0016746
GO:0016874
GO:0018858
GO:0018874
GO:0019395
GO:0019605
GO:0034641
GO:0042592
GO:0042632
GO:0043167
GO:0043226
GO:0044281
GO:0046872
GO:0047760
GO:0051186
GO:0070062
GO:0072562
GO:0102391
Hs.98732.0.S1_3p_at
ILMN_1661434
ILMN_1709539
PH_hs_0023661
TC16000929.hg
Participant Of
hasMember
xenobiotic/medium-chain fatty acid:CoA ligases [mitochondrial matrix]
Inferred To
Acsm1 [mitochondrial matrix] (Mus musculus)
ACSM1 [mitochondrial matrix] (Dictyostelium discoideum)
Homologues of ACSM1 [mitochondrial matrix] (Dictyostelium discoideum)
acsm3 [mitochondrial matrix] (Danio rerio)
acsm3 [mitochondrial matrix] (Xenopus tropicalis)
Cross References
RefSeq
NP_001305819.1
,
NP_443188.2
OpenTargets
ENSG00000166743
GeneCards
Q08AH1
HPA
ENSG00000166743-ACSM1
Ensembl
ENSP00000428650
,
ENSP00000428047
,
ENST00000519745
,
ENST00000307493
,
ENSG00000166743
,
ENSP00000301956
,
ENST00000520010
PRO
Q08AH1
HMDB Protein
HMDBP04188
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