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OxA-ARSI [endoplasmic reticulum lumen]
Stable Identifier
R-HSA-1614360
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
endoplasmic reticulum lumen
Synonyms
active ARSI, Arylsulfatase I, ARSI_HUMAN, ARSI
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Sphingolipid metabolism (Homo sapiens)
Glycosphingolipid metabolism (Homo sapiens)
Glycosphingolipid catabolism (Homo sapiens)
SUMF1 mediates the oxidation of cysteine to formylglycine, producing active arylsulfatases (Homo sapiens)
active ARS [endoplasmic reticulum lumen] (Homo sapiens)
OxA-ARSI [endoplasmic reticulum lumen] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Gamma carboxylation, hypusinylation, hydroxylation, and arylsulfatase activation (Homo sapiens)
The activation of arylsulfatases (Homo sapiens)
SUMF1 mediates the oxidation of cysteine to formylglycine, producing active arylsulfatases (Homo sapiens)
active ARS [endoplasmic reticulum lumen] (Homo sapiens)
OxA-ARSI [endoplasmic reticulum lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q5FYB1 ARSI
Gene Names
ARSI
Chain
signal peptide:1-23, chain:24-569
Reference Genes
BioGPS Gene:340075 ARSI
COSMIC (genes):ARSI ARSI
CTD Gene:340075 ARSI
dbSNP Gene:340075 ARSI
ENSEMBL:ENSG00000183876 ARSI
HGNC:32521 ARSI
KEGG:hsa:340075 ARSI
Monarch:340075 ARSI
NCBI Gene:340075 ARSI
OMIM:610009 ARSI
UCSC:Q5FYB1 ARSI
Reference Transcript
RefSeq:NM_001012301.3 ARSI
Other Identifiers
11726183_at
11726184_at
17001643
230275_PM_at
230275_at
2881352
2881353
2881354
2881355
2881356
2881357
2881358
2881359
2881360
340075
49241_at
8115144
A_23_P19030
GE541873
GO:0003824
GO:0004065
GO:0005515
GO:0005576
GO:0005783
GO:0005788
GO:0008484
GO:0016787
GO:0043226
GO:0046872
HMNXSV003055562
Hs.23871.0.A1_3p_at
ILMN_1727156
PH_hs_0033507
TC05001935.hg
Participates
as a member of
active ARS [endoplasmic reticulum lumen] (Homo sapiens)
Other forms of this molecule
ARSI [endoplasmic reticulum lumen]
Inferred To
arsi [endoplasmic reticulum lumen]
(Xenopus tropicalis)
ARSI [endoplasmic reticulum lumen]
(Bos taurus)
ARSI [endoplasmic reticulum lumen]
(Canis familiaris)
ARSI [endoplasmic reticulum lumen]
(Sus scrofa)
OxA-ARSI [endoplasmic reticulum lumen]
(Gallus gallus)
OxA-ARSI [endoplasmic reticulum lumen]
(Mus musculus)
OxA-ARSI [endoplasmic reticulum lumen]
(Rattus norvegicus)
sul-3 [endoplasmic reticulum lumen]
(Caenorhabditis elegans)
Modified Residues
Name
L-3-oxoalanine (Ser) at 93
Coordinate
93
PsiMod Name
L-3-oxoalanine (Ser)
PsiMod Definition
A protein modification that effectively converts an L-serine residue to L-oxoalanine.
Cross References
ENSEMBL
ENST00000515301
,
ENSP00000426879
,
ENSP00000333395
,
ENST00000328668
OpenTargets
ENSG00000183876
HPA
ENSG00000183876-ARSI
PRO
Q5FYB1
Pharos - Targets
Q5FYB1
GlyGen
Q5FYB1
Orphanet
ARSI
HMDB Protein
HMDBP07459
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P11021 HSPA5
6
HSPA5 [lumenal side of endoplasmic reticulum membrane]
(R-HSA-985498)
HSPA5 [nucleoplasm]
(R-HSA-5252042)
HSPA5 [cytosol]
(R-HSA-5252115)
HSPA5 [endoplasmic reticulum membrane]
(R-HSA-351315)
HSPA5 [endoplasmic reticulum lumen]
(R-HSA-387190)
HSPA5 [extracellular region]
(R-HSA-351322)
0.527
2
UniProt:Q9H8H0 NOL11
1
NOL11 [nucleoplasm]
(R-HSA-6790684)
0.527
2
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