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OxA-ARSD [endoplasmic reticulum lumen]
Stable Identifier
R-HSA-1614317
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
endoplasmic reticulum lumen
Synonyms
active ARSD, Arylsulfatase D, ARSD_HUMAN, ARSD
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Sphingolipid metabolism (Homo sapiens)
Glycosphingolipid metabolism (Homo sapiens)
Glycosphingolipid catabolism (Homo sapiens)
SUMF1 mediates the oxidation of cysteine to formylglycine, producing active arylsulfatases (Homo sapiens)
active ARS [endoplasmic reticulum lumen] (Homo sapiens)
OxA-ARSD [endoplasmic reticulum lumen] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Gamma carboxylation, hypusinylation, hydroxylation, and arylsulfatase activation (Homo sapiens)
The activation of arylsulfatases (Homo sapiens)
SUMF1 mediates the oxidation of cysteine to formylglycine, producing active arylsulfatases (Homo sapiens)
active ARS [endoplasmic reticulum lumen] (Homo sapiens)
OxA-ARSD [endoplasmic reticulum lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:P51689 ARSD
Gene Names
ARSD
Chain
signal peptide:1-33, chain:34-593
Reference Genes
BioGPS Gene:414 ARSD
COSMIC (genes):ARSD ARSD
CTD Gene:414 ARSD
dbSNP Gene:414 ARSD
ENSEMBL:ENSG00000006756 ARSD
HGNC:717 ARSD
KEGG:hsa:414 ARSD
Monarch:414 ARSD
NCBI Gene:414 ARSD
OMIM:300002 ARSD
UCSC:P51689 ARSD
Reference Transcript
RefSeq:NM_001669.3 ARSD
RefSeq:NM_009589.3 ARSD
Other Identifiers
11717369_a_at
11717370_at
11738344_at
17108779
206831_PM_s_at
206831_s_at
207784_PM_at
207784_at
223695_PM_s_at
223695_s_at
223696_PM_at
223696_at
225280_PM_x_at
225280_x_at
225286_PM_at
225286_at
230131_PM_x_at
230131_x_at
232423_PM_at
232423_at
3997739
3997740
3997741
3997742
3997743
3997744
3997745
3997746
3997749
3997750
3997752
3997753
3997754
3997755
3997756
3997757
3997758
3997759
3997760
3997762
3997764
3997765
3997768
3997769
4030014
4030015
414
41568_at
45286_at
47680_at
53066_at
79846_at
8171148
A_23_P217712
A_23_P357760
A_33_P3330099
GE58451
GO:0003824
GO:0004065
GO:0005764
GO:0005773
GO:0005788
GO:0016020
GO:0016787
GO:0043226
GO:0046872
HMNXSV003016834
HMNXSV003024613
HMNXSV003028446
Hs.19978.5.S1_3p_a_at
Hs.19978.5.S2_3p_at
Hs.307755.0.S1_3p_at
ILMN_1661624
ILMN_1684873
ILMN_1684956
PH_hs_0028201
TC0X000805.hg
X83572_at
g4502238_3p_s_at
g6806884_3p_at
Participates
as a member of
active ARS [endoplasmic reticulum lumen] (Homo sapiens)
Other forms of this molecule
ARSD [endoplasmic reticulum lumen]
Inferred To
OxA-ARSD [endoplasmic reticulum lumen]
(Bos taurus)
OxA-ARSD [endoplasmic reticulum lumen]
(Gallus gallus)
OxA-ARSD [endoplasmic reticulum lumen]
(Schizosaccharomyces pombe)
arsd [endoplasmic reticulum lumen]
(Xenopus tropicalis)
ARSL [endoplasmic reticulum lumen]
(Canis familiaris)
ARSD [endoplasmic reticulum lumen]
(Sus scrofa)
Homologues of OxA-ARSD [endoplasmic reticulum lumen]
(Gallus gallus)
LOC418658 [endoplasmic reticulum lumen]
(Gallus gallus)
Modified Residues
Name
L-3-oxoalanine (Ser) at 89
Coordinate
89
PsiMod Name
L-3-oxoalanine (Ser)
PsiMod Definition
A protein modification that effectively converts an L-serine residue to L-oxoalanine.
Cross References
ENSEMBL
ENST00000381154
,
ENSP00000370546
OpenTargets
ENSG00000006756
HPA
ENSG00000006756-ARSD
PRO
P51689
Pharos - Targets
P51689
GlyGen
P51689
HMDB Protein
HMDBP00316
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