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GM2A:GM2 [lysosomal lumen]
Stable Identifier
R-HSA-1605600
Type
Complex
Species
Homo sapiens
Compartment
lysosomal lumen
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Sphingolipid metabolism (Homo sapiens)
Glycosphingolipid metabolism (Homo sapiens)
Ganglioside GM2 activator presents GM2 to hexosaminidase for cleavage (Homo sapiens)
GM2A:GM2 [lysosomal lumen] (Homo sapiens)
Hexosaminidase A cleaves GalNAc from GM2 to form GM3 (Homo sapiens)
GM2A:GM2 [lysosomal lumen] (Homo sapiens)
Participants
components
GM2 [lysosomal lumen]
GM2A(32-193) [lysosomal lumen]
(Homo sapiens)
Participates
as an output of
Ganglioside GM2 activator presents GM2 to hexosaminidase for cleavage (Homo sapiens)
as an input of
Hexosaminidase A cleaves GalNAc from GM2 to form GM3 (Homo sapiens)
Inferred To
GM2A:GM2 [lysosomal lumen]
(Bos taurus)
GM2A:GM2 [lysosomal lumen]
(Caenorhabditis elegans)
GM2A:GM2 [lysosomal lumen]
(Canis familiaris)
GM2A:GM2 [lysosomal lumen]
(Danio rerio)
GM2A:GM2 [lysosomal lumen]
(Mus musculus)
GM2A:GM2 [lysosomal lumen]
(Rattus norvegicus)
GM2A:GM2 [lysosomal lumen]
(Sus scrofa)
GM2A:GM2 [lysosomal lumen]
(Xenopus tropicalis)
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