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SUCLA2 [mitochondrial matrix]
Stable Identifier
R-HSA-156624
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Succinyl-CoA synthetase, betaA chain
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Citric acid cycle (TCA cycle) (Homo sapiens)
SUCLG1/A2 cleaves succinyl-CoA (Homo sapiens)
SUCLA2:SUCLG1 [mitochondrial matrix] (Homo sapiens)
SUCLA2:Mg2+ [mitochondrial matrix] (Homo sapiens)
SUCLA2 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9P2R7 SUCLA2
Gene Names
SUCLA2
Chain
transit peptide:1-52, chain:53-463
Reference Genes
BioGPS Gene:8803 SUCLA2
COSMIC (genes):SUCLA2 SUCLA2
CTD Gene:8803 SUCLA2
dbSNP Gene:8803 SUCLA2
ENSEMBL:ENSG00000136143 SUCLA2
HGNC:11448 SUCLA2
KEGG:hsa:8803 SUCLA2
Monarch:8803 SUCLA2
NCBI Gene:8803 SUCLA2
OMIM:603921 SUCLA2
UCSC:Q9P2R7 SUCLA2
Reference Transcript
RefSeq:NM_003850.3 SUCLA2
Other Identifiers
11748619_a_at
11748620_x_at
11755266_x_at
11755492_a_at
11759519_a_at
16778956
16778959
202930_PM_s_at
202930_s_at
2544609
2901605
3513309
3513310
3513311
3513315
3513317
3513318
3513321
3513323
3513324
3513325
3513326
3513327
3513328
3513329
3513331
3513332
3513333
3513334
3513335
3513336
3513337
3513340
3513343
3513344
3513345
3513346
3513347
3513348
3513350
3513351
3513352
3513353
3513354
3513355
3513356
3513357
3513362
3513364
3513372
3513373
3513377
3513379
3513381
3513382
40893_at
71150_r_at
76636_at
7971541
84409_i_at
8803
A_21_P0008255
A_21_P0011228
A_23_P117157
GE683287
GO:0000166
GO:0000287
GO:0003824
GO:0004775
GO:0005515
GO:0005524
GO:0005737
GO:0005739
GO:0005759
GO:0006099
GO:0006104
GO:0006781
GO:0006790
GO:0009361
GO:0016874
GO:0042709
GO:0043226
GO:0046872
GO:0055086
GO:0070062
GO:1901135
GO:1901289
HMNXSV003007310
HMNXSV003019074
HMNXSV003050089
ILMN_1660787
PH_hs_0010761
TC13000651.hg
TC13000652.hg
TC13001485.hg
g11321582_3p_a_at
p19043
p4039
Participates
as a component of
SUCLA2:Mg2+ [mitochondrial matrix] (Homo sapiens)
Inferred To
LSC2 [mitochondrial matrix]
(Saccharomyces cerevisiae)
ScsbetaA [mitochondrial matrix]
(Drosophila melanogaster)
SUCLA2 [mitochondrial matrix]
(Bos taurus)
SUCLA2 [mitochondrial matrix]
(Canis familiaris)
SUCLA2 [mitochondrial matrix]
(Gallus gallus)
SUCLA2 [mitochondrial matrix]
(Plasmodium falciparum)
SUCLA2 [mitochondrial matrix]
(Schizosaccharomyces pombe)
SUCLA2 [mitochondrial matrix]
(Sus scrofa)
scsC [mitochondrial matrix]
(Dictyostelium discoideum)
sucla2 [mitochondrial matrix]
(Danio rerio)
sucla2 [mitochondrial matrix]
(Xenopus tropicalis)
suca-1 [mitochondrial matrix]
(Caenorhabditis elegans)
Sucla2 [mitochondrial matrix]
(Mus musculus)
Sucla2 [mitochondrial matrix]
(Rattus norvegicus)
Cross References
RefSeq
NP_003841.1
ENSEMBL
ENST00000643584
,
ENST00000646932
,
ENSP00000494360
,
ENSG00000136143
,
ENSP00000494987
OpenTargets
ENSG00000136143
GeneCards
SUCLA2
HPA
ENSG00000136143-SUCLA2
PRO
Q9P2R7
Pharos - Targets
Q9P2R7
GlyGen
Q9P2R7
Orphanet
SUCLA2
HMDB Protein
HMDBP00971
PDB
6G4Q
Interactors (4)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q96CV9 OPTN
6
p-S177,S473,S513-OPTN [cytosol]
(R-HSA-9687840)
OPTN [cytosol]
(R-HSA-9687907)
p-S177-OPTN [cytosol]
(R-HSA-2562525)
p-S177-OPTN [nucleoplasm]
(R-HSA-2562595)
OPTN [Golgi membrane]
(R-HSA-2161111)
OPTN [recycling endosome membrane]
(R-HSA-8854141)
0.556
3
UniProt:Q9UBN6 TNFRSF10D
1
TNFRSF10D [plasma membrane]
(R-HSA-5633374)
0.556
3
UniProt:Q15436 SEC23A
4
SEC23A [endoplasmic reticulum membrane]
(R-HSA-203976)
SEC23A [cytosol]
(R-HSA-203972)
SEC23A [ER to Golgi transport vesicle membrane]
(R-HSA-204024)
p-S738,T744 SEC23A [cytosol]
(R-HSA-5685740)
0.556
3
UniProt:P13569 CFTR
17
misfolded CFTR [endoplasmic reticulum membrane]
(R-HSA-8868730)
CFTR [endoplasmic reticulum membrane]
(R-HSA-8866837)
CFTR [plasma membrane]
(R-HSA-383188)
CFTR N1303K [plasma membrane]
(R-HSA-5678983)
CFTR F508del [plasma membrane]
(R-HSA-5678978)
CFTR W1282* [plasma membrane]
(R-HSA-5678976)
CFTR G551D [plasma membrane]
(R-HSA-5678977)
CFTR G542* [plasma membrane]
(R-HSA-5678986)
ub-CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866842)
ub-CFTR F508del [cytosol]
(R-HSA-8866838)
CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866834)
PolyUb-CFTR [endosome membrane]
(R-HSA-6782976)
CFTR [endosome membrane]
(R-HSA-6782965)
CFTR [Golgi-associated vesicle membrane]
(R-HSA-5627079)
CFTR [lysosomal membrane]
(R-HSA-5627279)
PolyUb-CFTR [plasma membrane]
(R-HSA-8867595)
PolyUb-CFTR [clathrin-coated endocytic vesicle membrane]
(R-HSA-8869104)
0.483
8
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