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COX17 [mitochondrial intermembrane space]
Stable Identifier
R-HSA-1307788
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial intermembrane space
Synonyms
Cytochrome c oxidase copper chaperone, COX17_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex IV assembly (Homo sapiens)
Metallochaperone inserts 2Cu2+ into MT-CO2 (Homo sapiens)
COX17 [mitochondrial intermembrane space] (Homo sapiens)
COX17:Cu [mitochondrial intermembrane space] (Homo sapiens)
COX17 [mitochondrial intermembrane space] (Homo sapiens)
Metallochaperone inserts Cu2+ into MT-CO1 (Homo sapiens)
COX17 [mitochondrial intermembrane space] (Homo sapiens)
COX17:Cu [mitochondrial intermembrane space] (Homo sapiens)
COX17 [mitochondrial intermembrane space] (Homo sapiens)
Protein localization (Homo sapiens)
Mitochondrial protein import (Homo sapiens)
MIA40:ERV1 (CHCHD4:GFER) oxidizes cysteine residues to cystine disulfide bonds (Homo sapiens)
Substrates of MIA40:ERV1 [mitochondrial intermembrane space] (Homo sapiens)
COX17 [mitochondrial intermembrane space] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q14061 COX17
Gene Names
COX17
Chain
initiator methionine:, chain:2-63
Reference Genes
BioGPS Gene:10063 COX17
COSMIC (genes):COX17 COX17
CTD Gene:10063 COX17
dbSNP Gene:10063 COX17
ENSEMBL:ENSG00000138495 COX17
HGNC:2264 COX17
KEGG:hsa:10063 COX17
Monarch:10063 COX17
NCBI Gene:10063 COX17
OMIM:604813 COX17
UCSC:Q14061 COX17
Reference Transcript
RefSeq:NM_005694.1 COX17
Other Identifiers
10063
11757627_at
203880_PM_at
203880_at
2690969
2690970
2690974
2690981
2690984
2690985
2690986
2690987
2690988
2690990
2690991
2690992
2690994
3488593
40427_at
7968972
8089795
A_23_P144244
A_23_P65157
GE57799
GE86319
GO:0005507
GO:0005515
GO:0005737
GO:0005739
GO:0005758
GO:0006091
GO:0006825
GO:0008047
GO:0008284
GO:0016531
GO:0033617
GO:0043226
GO:0046872
GO:0065003
GO:0098772
GO:0140104
GO:1903136
GO:1904960
HMNXSV003033293
ILMN_2187718
L77701_at
PH_hs_0035365
TC03003390.hg
g5031644_3p_at
Participates
as a candidate of
Substrates of MIA40:ERV1 [mitochondrial intermembrane space] (Homo sapiens)
as an output of
Metallochaperone inserts Cu2+ into MT-CO1 (Homo sapiens)
Metallochaperone inserts 2Cu2+ into MT-CO2 (Homo sapiens)
as a component of
COX17:Cu [mitochondrial intermembrane space] (Homo sapiens)
Other forms of this molecule
4xHC-COX17 [mitochondrial intermembrane space]
Inferred To
cox17 [mitochondrial intermembrane space]
(Danio rerio)
cox17 [mitochondrial intermembrane space]
(Xenopus tropicalis)
COX17 [mitochondrial intermembrane space]
(Bos taurus)
COX17 [mitochondrial intermembrane space]
(Canis familiaris)
COX17 [mitochondrial intermembrane space]
(Dictyostelium discoideum)
COX17 [mitochondrial intermembrane space]
(Gallus gallus)
COX17 [mitochondrial intermembrane space]
(Mus musculus)
COX17 [mitochondrial intermembrane space]
(Plasmodium falciparum)
COX17 [mitochondrial intermembrane space]
(Saccharomyces cerevisiae)
COX17 [mitochondrial intermembrane space]
(Schizosaccharomyces pombe)
COX17 [mitochondrial intermembrane space]
(Sus scrofa)
cox-17 [mitochondrial intermembrane space]
(Caenorhabditis elegans)
Cox17 [mitochondrial intermembrane space]
(Drosophila melanogaster)
Cross References
ENSEMBL
ENSG00000138495
,
ENSP00000261070
,
ENST00000497116
,
ENST00000261070
,
ENST00000468918
,
ENSP00000417805
,
ENSP00000417923
OpenTargets
ENSG00000138495
GeneCards
COX17
HPA
ENSG00000138495-COX17
PRO
Q14061
Pharos - Targets
Q14061
HMDB Protein
HMDBP08243
PDB
2LGQ
,
2RNB
,
2L0Y
,
2RN9
Interactors (5)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q9BW62 KATL1
0.666
4
UniProt:O75880 SCO1
1
SCO1 [mitochondrial inner membrane]
(R-HSA-5336170)
0.66
3
UniProt:Q8N4Q1-1 CHCHD4
0.558
2
UniProt:Q7Z699 SPRED1
2
SPRED1 [plasma membrane]
(R-HSA-5658225)
SPRED1 [cytosol]
(R-HSA-5654207)
0.556
3
UniProt:P60410 KRTAP10-8
1
KRTAP10-8 [cytosol]
(R-HSA-6810301)
0.556
3
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