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PMPCA [mitochondrial inner membrane]
Stable Identifier
R-HSA-1299450
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Mitochondrial-processing peptidase subunit alpha, MPPA_HUMAN
Locations in the PathwayBrowser
Expand all
Protein localization (Homo sapiens)
Mitochondrial protein import (Homo sapiens)
MPP cleaves targeting peptide (presequence) of inner membrane precursors (Homo sapiens)
Mitochondrial processing peptidase [mitochondrial inner membrane] (Homo sapiens)
PMPCA [mitochondrial inner membrane] (Homo sapiens)
MPP cleaves targeting peptide (presequence) of matrix precursors (Homo sapiens)
Mitochondrial processing peptidase [mitochondrial inner membrane] (Homo sapiens)
PMPCA [mitochondrial inner membrane] (Homo sapiens)
Transport of small molecules (Homo sapiens)
Mitochondrial calcium ion transport (Homo sapiens)
Processing of SMDT1 (Homo sapiens)
PMPCA:PMPCB cleaves the transit peptide of proSMDT1 (proEMRE) (Homo sapiens)
Mitochondrial processing peptidase [mitochondrial inner membrane] (Homo sapiens)
PMPCA [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q10713 PMPCA
Gene Names
PMPCA, INPP5E, KIAA0123, MPPA
Chain
transit peptide:1-33, chain:34-525
Reference Genes
BioGPS Gene:23203 PMPCA
COSMIC (genes):PMPCA PMPCA
CTD Gene:23203 PMPCA
dbSNP Gene:23203 PMPCA
ENSEMBL:ENSG00000165688 PMPCA
HGNC:18667 PMPCA
KEGG Gene (Homo sapiens):23203 PMPCA
Monarch:23203 PMPCA
NCBI Gene:23203 PMPCA
OMIM:613036 PMPCA
UCSC:Q10713 PMPCA
Reference Transcript
RefSeq:NM_001282944.1 PMPCA
RefSeq:NM_001282946.1 PMPCA
RefSeq:NM_015160.2 PMPCA
Other Identifiers
0005550091
11748770_a_at
17091239
212088_at
23203
2778014
3194339
3194340
3194342
3194344
3194347
3194351
3194355
3194356
3194357
3194358
3194359
3194360
3194363
3194371
3194372
36602_at
8159337
A_23_P32125
D50913_at
GE80602
GO:0003674
GO:0003824
GO:0004175
GO:0004222
GO:0005515
GO:0005575
GO:0005576
GO:0005615
GO:0005622
GO:0005737
GO:0005739
GO:0005743
GO:0005759
GO:0006508
GO:0006605
GO:0006627
GO:0006810
GO:0006851
GO:0007005
GO:0008150
GO:0008233
GO:0015031
GO:0016020
GO:0017087
GO:0032991
GO:0043167
GO:0043226
GO:0046872
GO:0051604
GO:0055085
Hs.75353.0.A1_3p_at
ILMN_1764239
PH_hs_0004318
TC09000812.hg
Participant Of
hasComponent
Mitochondrial processing peptidase [mitochondrial inner membrane]
Inferred To
pmpca [mitochondrial inner membrane] (Danio rerio)
pmpca [mitochondrial inner membrane] (Xenopus tropicalis)
CG8728-RA [mitochondrial inner membrane] (Drosophila melanogaster)
mppa-1 [mitochondrial inner membrane] (Caenorhabditis elegans)
PMPCA [mitochondrial inner membrane] (Canis familiaris)
PMPCA [mitochondrial inner membrane] (Gallus gallus)
PMPCA [mitochondrial inner membrane] (Sus scrofa)
Pmpca [mitochondrial inner membrane] (Mus musculus)
Pmpca [mitochondrial inner membrane] (Rattus norvegicus)
Cross References
RefSeq
NP_055975.1
,
NP_001269873.1
,
NP_001269875.1
Target Pathogen
5b354852be737e166372ecb7
OpenTargets
ENSG00000165688
HPA
ENSG00000165688-PMPCA
GeneCards
Q10713
Ensembl
ENSG00000165688
,
ENSP00000416702
,
ENST00000399219
,
ENSP00000360782
,
ENST00000371717
PRO
Q10713
Orphanet
23282
HMDB Protein
HMDBP02210
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q80H93 8b
1
8b [cytosol]
(R-COV-9678168)
0.527
2
UniProt:P0DTC5 M
8
N-glycan M [endocytic vesicle membrane]
(R-COV-9694738)
M [endocytic vesicle membrane]
(R-COV-9694563)
N-glycan M [endoplasmic reticulum membrane]
(R-COV-9694684)
nascent M [endoplasmic reticulum lumen]
(R-COV-9694279)
N-glycan M [endoplasmic reticulum-Golgi intermediate compartment membrane]
(R-COV-9694446)
M [endoplasmic reticulum-Golgi intermediate compartment membrane]
(R-COV-9694439)
M [virion membrane]
(R-COV-9694320)
N-glycan M [virion membrane]
(R-COV-9694385)
0.527
2
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