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PMPCB [mitochondrial inner membrane]
Stable Identifier
R-HSA-1299434
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Mitochondrial-processing peptidase subunit beta, MPPB_HUMAN
Locations in the PathwayBrowser
Expand all
Protein localization (Homo sapiens)
Mitochondrial protein import (Homo sapiens)
MPP cleaves targeting peptide (presequence) of inner membrane precursors (Homo sapiens)
Mitochondrial processing peptidase [mitochondrial inner membrane] (Homo sapiens)
PMPCB [mitochondrial inner membrane] (Homo sapiens)
PMPCB [mitochondrial inner membrane] (Homo sapiens)
MPP cleaves targeting peptide (presequence) of matrix precursors (Homo sapiens)
Mitochondrial processing peptidase [mitochondrial inner membrane] (Homo sapiens)
PMPCB [mitochondrial inner membrane] (Homo sapiens)
PMPCB [mitochondrial inner membrane] (Homo sapiens)
Transport of small molecules (Homo sapiens)
Mitochondrial calcium ion transport (Homo sapiens)
Processing of SMDT1 (Homo sapiens)
PMPCA:PMPCB cleaves the transit peptide of proSMDT1 (proEMRE) (Homo sapiens)
Mitochondrial processing peptidase [mitochondrial inner membrane] (Homo sapiens)
PMPCB [mitochondrial inner membrane] (Homo sapiens)
PMPCB [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O75439 PMPCB
Gene Names
PMPCB, MPPB
Chain
transit peptide:1-43, chain:44-489
Reference Genes
BioGPS Gene:9512 PMPCB
COSMIC (genes):PMPCB PMPCB
CTD Gene:9512 PMPCB
dbSNP Gene:9512 PMPCB
ENSEMBL:ENSG00000105819.14 PMPCB
HGNC:9119 PMPCB
KEGG Gene (Homo sapiens):9512 PMPCB
Monarch:9512 PMPCB
NCBI Gene:9512 PMPCB
OMIM:603131 PMPCB
UCSC:O75439 PMPCB
Reference Transcript
RefSeq:NM_004279.2 PMPCB
Other Identifiers
0000050632
11732121_a_at
11732122_at
17049939
201682_PM_at
201682_at
244534_PM_at
244534_at
3017155
3017156
3017157
3017158
3017161
3017163
3017164
3017166
3017167
3017169
3017171
3017173
3017175
3017177
3017178
3017179
3017180
3017181
3017182
3017183
3017184
3017185
32167_at
8135235
83021_s_at
83022_r_at
9512
A_14_P137807
A_23_P134464
A_33_P3294162
GE61431
GE81374
GO:0004175
GO:0004222
GO:0005622
GO:0005737
GO:0005739
GO:0005743
GO:0005759
GO:0006508
GO:0006627
GO:0006851
GO:0006886
GO:0007005
GO:0008233
GO:0008237
GO:0016485
GO:0016787
GO:0017087
GO:0032991
GO:0043226
GO:0046872
GO:0051604
GO:0055085
GO:0140096
HMNXSV003006747
Hs.147877.0.A1_3p_at
ILMN_1728660
PH_hs_0010853
TC07000672.hg
g4758733_3p_at
Participates
as a component of
Mitochondrial processing peptidase [mitochondrial inner membrane] (Homo sapiens)
Inferred To
UQCR-C1 [mitochondrial inner membrane]
(Drosophila melanogaster)
PMPCB [mitochondrial inner membrane]
(Bos taurus)
PMPCB [mitochondrial inner membrane]
(Caenorhabditis elegans)
PMPCB [mitochondrial inner membrane]
(Canis familiaris)
PMPCB [mitochondrial inner membrane]
(Danio rerio)
PMPCB [mitochondrial inner membrane]
(Gallus gallus)
PMPCB [mitochondrial inner membrane]
(Mus musculus)
PMPCB [mitochondrial inner membrane]
(Rattus norvegicus)
PMPCB [mitochondrial inner membrane]
(Sus scrofa)
Cross References
RefSeq
NP_004270.2
OpenTargets
ENSG00000105819
GeneCards
O75439
HPA
ENSG00000105819-PMPCB
Ensembl
ENST00000249269
,
ENSP00000249269
,
ENSG00000105819
PRO
O75439
Pharos - Targets
O75439
Orphanet
28749
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P0DTC5 M
10
M [plasma membrane]
(R-COV-9755780)
N-glycan M [virion membrane]
(R-COV-9694385)
M [virion membrane]
(R-COV-9694320)
M [endocytic vesicle membrane]
(R-COV-9694563)
N-glycan M [endocytic vesicle membrane]
(R-COV-9694738)
M [endoplasmic reticulum-Golgi intermediate compartment membrane]
(R-COV-9694439)
N-glycan M [endoplasmic reticulum-Golgi intermediate compartment membrane]
(R-COV-9694446)
M [endoplasmic reticulum membrane]
(R-COV-9767620)
nascent M [endoplasmic reticulum lumen]
(R-COV-9694279)
N-glycan M [endoplasmic reticulum membrane]
(R-COV-9694684)
0.643
3
UniProt:Q80H93 8b
1
8b [cytosol]
(R-COV-9678168)
0.527
2
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