Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
MTX2 [mitochondrial outer membrane]
Stable Identifier
R-HSA-1252142
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial outer membrane
Synonyms
Metaxin-2, MTX2_HUMAN
Locations in the PathwayBrowser
Expand all
Organelle biogenesis and maintenance (Homo sapiens)
Mitochondrial biogenesis (Homo sapiens)
Cristae formation (Homo sapiens)
Formation of MIB complex containing the MICOS complex causes curvature of mitochondrial inner membrane (Homo sapiens)
MIB [mitochondrial inner membrane] (Homo sapiens)
SAM complex [mitochondrial outer membrane] (Homo sapiens)
MTX2 [mitochondrial outer membrane] (Homo sapiens)
SAM complex [mitochondrial outer membrane] (Homo sapiens)
MTX2 [mitochondrial outer membrane] (Homo sapiens)
Protein localization (Homo sapiens)
Mitochondrial protein import (Homo sapiens)
SAM50 complex inserts proteins into mitochondrial outer membrane (Homo sapiens)
SAM complex [mitochondrial outer membrane] (Homo sapiens)
MTX2 [mitochondrial outer membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O75431 MTX2
Gene Names
MTX2
Chain
initiator methionine:, chain:2-263
Reference Genes
BioGPS Gene:10651 MTX2
COSMIC (genes):MTX2 MTX2
CTD Gene:10651 MTX2
dbSNP Gene:10651 MTX2
ENSEMBL:ENSG00000128654 MTX2
HGNC:7506 MTX2
KEGG:hsa:10651 MTX2
Monarch:10651 MTX2
NCBI Gene:10651 MTX2
OMIM:608555 MTX2
UCSC:O75431 MTX2
Reference Transcript
RefSeq:NM_001006635.2 MTX2
RefSeq:NM_001319098.1 MTX2
RefSeq:NM_006554.4 MTX2
RefSeq:NM_001319097.1 MTX2
Other Identifiers
10651
11730835_a_at
16887993
203517_PM_at
203517_at
2517014
2517015
2517017
2517020
2517021
2517022
2517033
2517036
2517037
2517038
2517039
2517040
2517045
2517046
2517047
2517048
2517049
2517050
35642_at
8046573
A_14_P122048
A_23_P120335
GE54492
GO:0001401
GO:0005515
GO:0005730
GO:0005737
GO:0005739
GO:0005741
GO:0006839
GO:0006886
GO:0007005
GO:0007007
GO:0015031
GO:0016020
GO:0043226
GO:0045040
GO:0061024
GO:0140275
HMNXSV003041142
ILMN_1794046
ILMN_1799466
ILMN_2306565
PH_hs_0002684
PH_hs_0031139
TC02001057.hg
TC02003706.hg
g5729936_3p_at
Participates
as a component of
SAM complex [mitochondrial outer membrane] (Homo sapiens)
Cross References
ENSEMBL
ENSP00000249442
,
ENST00000249442
OpenTargets
ENSG00000128654
HPA
ENSG00000128654-MTX2
PRO
O75431
Pharos - Targets
O75431
Interactors (6)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q9NX63 CHCHD3
3
CHCHD3 [mitochondrial intermembrane space]
(R-HSA-8874907)
4xHC-CHCHD3 [mitochondrial intermembrane space]
(R-HSA-8874910)
CHCHD3 (MIC19) [mitochondrial inner membrane]
(R-HSA-8949583)
0.643
4
UniProt:Q9BRQ6 CHCHD6
1
CHCHD6 (MIC25) [mitochondrial inner membrane]
(R-HSA-8949568)
0.643
4
UniProt:Q16891 IMMT
1
IMMT (MIC60) [mitochondrial inner membrane]
(R-HSA-8949569)
0.643
4
UniProt:O75478 TADA2A
1
TADA2A [nucleoplasm]
(R-HSA-3662284)
0.556
3
UniProt:Q15669 RHOH
1
RHOH [plasma membrane]
(R-HSA-194859)
0.556
3
UniProt:Q6UXV4 APOOL
3
APOOL (MIC27) [mitochondrial inner membrane]
(R-HSA-8949612)
APOOL [extracellular region]
(R-HSA-8862979)
APOOL [platelet alpha granule lumen]
(R-HSA-8863003)
0.527
4
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text