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fh [mitochondrial matrix]
Stable Identifier
R-DME-1362390
Type
Protein [EntityWithAccessionedSequence]
Species
Drosophila melanogaster
Compartment
mitochondrial matrix
Synonyms
FXN(81-210), Q9W385
Locations in the PathwayBrowser
Expand all
Metabolism (Drosophila melanogaster)
Aerobic respiration and respiratory electron transport (Drosophila melanogaster)
Citric acid cycle (TCA cycle) (Drosophila melanogaster)
Maturation of TCA enzymes and regulation of TCA cycle (Drosophila melanogaster)
Frataxin transfers Fe2+ to ACO2 (Drosophila melanogaster)
2 Iron:FXN [mitochondrial matrix] (Drosophila melanogaster)
fh [mitochondrial matrix] (Drosophila melanogaster)
fh [mitochondrial matrix] (Drosophila melanogaster)
Respiratory electron transport (Drosophila melanogaster)
Complex III assembly (Drosophila melanogaster)
2Fe-2S is inserted in UQCRFS1 (Drosophila melanogaster)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Drosophila melanogaster)
fh [mitochondrial matrix] (Drosophila melanogaster)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Drosophila melanogaster)
fh [mitochondrial matrix] (Drosophila melanogaster)
fh [mitochondrial matrix] (Drosophila melanogaster)
Mitochondrial iron-sulfur cluster biogenesis (Drosophila melanogaster)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Drosophila melanogaster)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Drosophila melanogaster)
2 Iron:FXN [mitochondrial matrix] (Drosophila melanogaster)
fh [mitochondrial matrix] (Drosophila melanogaster)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Drosophila melanogaster)
fh [mitochondrial matrix] (Drosophila melanogaster)
Frataxin binds iron (Drosophila melanogaster)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Drosophila melanogaster)
2 Iron:FXN [mitochondrial matrix] (Drosophila melanogaster)
fh [mitochondrial matrix] (Drosophila melanogaster)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Drosophila melanogaster)
fh [mitochondrial matrix] (Drosophila melanogaster)
External Reference Information
External Reference
UniProt:Q9W385
Gene Names
fh
Reference Genes
BioGPS Gene:31845 fh
ENSEMBL:FBgn0030092
FlyBase:FBgn0030092
KEGG:dme:Dmel_CG8971 fh
Monarch:31845 fh
NCBI Gene:31845 fh
UCSC:Q9W385 fh
Reference Transcript
RefSeq:NM_078539.3 fh
Other Identifiers
144731_at
1639567_at
31845
GO:0003824
GO:0004322
GO:0005739
GO:0005759
GO:0006629
GO:0006694
GO:0006783
GO:0006811
GO:0006826
GO:0006879
GO:0006979
GO:0007018
GO:0008198
GO:0008199
GO:0008340
GO:0008344
GO:0010039
GO:0016042
GO:0016226
GO:0016491
GO:0018283
GO:0019896
GO:0034986
GO:0042542
GO:0043226
GO:0045823
GO:0045998
GO:0051537
GO:0051881
GO:0099128
GO:0140104
GO:1903862
GO:1904115
GO:1990221
Participates
as an output of
Frataxin transfers Fe2+ to ACO2 (Drosophila melanogaster)
as a component of
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Drosophila melanogaster)
2 Iron:FXN [mitochondrial matrix] (Drosophila melanogaster)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Drosophila melanogaster)
Inferred From
FXN(81-210) [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_511094.1
ENSEMBL
FBpp0071283
,
FBtr0071348
PRO
Q9W385
PDB
7N9I
Interactors (5)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q8IP15 Q8IP15
0.488
2
UniProt:O46070 O46070
0.488
2
UniProt:Q86BS3 Q86BS3
0.488
2
UniProt:Q9VAY6
1
BCAS2 [nucleoplasm]
(R-DME-5420902)
0.488
2
UniProt:P61857
3
TUBB8 [cytosol]
(R-DME-6805243)
TUBB1 [cytosol]
(R-DME-191703)
TUBB2A [cytosol]
(R-DME-191699)
0.488
2
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