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PCCB [mitochondrial matrix]
Stable Identifier
R-CFA-3323190
Type
Protein [EntityWithAccessionedSequence]
Species
Canis familiaris
Compartment
mitochondrial matrix
Synonyms
PCCB, A0A8I3S1S6
Locations in the PathwayBrowser
Expand all
Metabolism (Canis familiaris)
Metabolism of lipids (Canis familiaris)
Fatty acid metabolism (Canis familiaris)
Mitochondrial Fatty Acid Beta-Oxidation (Canis familiaris)
Propionyl-CoA catabolism (Canis familiaris)
propionyl-CoA + CO2 + ATP <=> D-methylmalonyl-CoA + ADP + orthophosphate (Canis familiaris)
6x(Btn-PCCA:PCCB) [mitochondrial matrix] (Canis familiaris)
Btn-PCCA:PCCB [mitochondrial matrix] (Canis familiaris)
PCCB [mitochondrial matrix] (Canis familiaris)
Metabolism of vitamins and cofactors (Canis familiaris)
Metabolism of water-soluble vitamins and cofactors (Canis familiaris)
Biotin transport and metabolism (Canis familiaris)
Cytoslic carboxylases translocate to mitochondrial matrix (Canis familiaris)
hCBXs [mitochondrial matrix] (Canis familiaris)
6x(Btn-PCCA:PCCB) [mitochondrial matrix] (Canis familiaris)
Btn-PCCA:PCCB [mitochondrial matrix] (Canis familiaris)
PCCB [mitochondrial matrix] (Canis familiaris)
Metabolism of proteins (Canis familiaris)
Mitochondrial protein degradation (Canis familiaris)
LONP1 binds mitochondrial matrix proteins (Canis familiaris)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Canis familiaris)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Canis familiaris)
PCCB [mitochondrial matrix] (Canis familiaris)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Canis familiaris)
PCCB [mitochondrial matrix] (Canis familiaris)
LONP1 degrades mitochondrial matrix proteins (Canis familiaris)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Canis familiaris)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Canis familiaris)
PCCB [mitochondrial matrix] (Canis familiaris)
External Reference Information
External Reference
UniProt:A0A8I3S1S6
Gene Names
PCCB
Reference Genes
BioGPS Gene:477076 PCCB
ENSEMBL:ENSCAFG00845020335.1
ENSEMBL_canis_lupus_familiaris_GENE:ENSCAFG00845020335.1 PCCB
KEGG Gene (Canis lupus familiaris):477076 PCCB
Monarch:477076 PCCB
NCBI Gene:477076 PCCB
Reference Transcript
RefSeq:XM_005634463.2 PCCB
Other Identifiers
477076
Cfa.10800.1.A1_at
Cfa.18014.1.S1_s_at
CfaAffx.11739.1.S1_s_at
GO:0003824
GO:0004658
GO:0005739
GO:0005759
GO:0016874
GO:0043226
GO:1902494
Participates
as a member of
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Canis familiaris)
as a component of
Btn-PCCA:PCCB [mitochondrial matrix] (Canis familiaris)
Other forms of this molecule
PCCB [cytosol]
Inferred From
PCCB [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
XP_005634520.1
OpenTargets
ENSG00000114054
Ensembl
ENSCAFT00845036139
,
ENSCAFP00845028279
,
ENSCAFG00845020335
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