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frh-1 [mitochondrial matrix]
Stable Identifier
R-CEL-1362390
Type
Protein [EntityWithAccessionedSequence]
Species
Caenorhabditis elegans
Compartment
mitochondrial matrix
Synonyms
FXN(81-210), Q9TY03
Locations in the PathwayBrowser
Expand all
Metabolism (Caenorhabditis elegans)
Mitochondrial iron-sulfur cluster biogenesis (Caenorhabditis elegans)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Caenorhabditis elegans)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Caenorhabditis elegans)
2 Iron:FXN [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
Frataxin binds iron (Caenorhabditis elegans)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Caenorhabditis elegans)
2 Iron:FXN [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
External Reference Information
External Reference
UniProt:Q9TY03
Gene Names
frh-1
Reference Genes
BioGPS Gene:174002 frh-1
ENSEMBL:WBGene00001486
KEGG Gene (Caenorhabditis elegans):CELE_F59G1.7 frh-1
Monarch:174002 frh-1
NCBI Gene:174002 frh-1
UCSC:Q9TY03 frh-1
Wormbase:WBGene00001486
Reference Transcript
RefSeq:NM_062782.3 frh-1
Other Identifiers
174002
18485685
187488_at
A_12_P120338
CE19476
CE_WBGene00001486_A
CE_WBGene00001486_B
CE_WBGene00001486_C
CGZ0025688
F59G1.7
F59G1.7_107-166_0.917_7_B
F59G1.7_252-311_0.946_4_A
F59G1.7_315-374_0.969_1_C
F59G1_7P00036
F59G1_7P00168
F59G1_7P00304
GO:0003674
GO:0004322
GO:0005575
GO:0005622
GO:0005737
GO:0005739
GO:0006790
GO:0008150
GO:0008199
GO:0016226
GO:0016491
GO:0022607
GO:0043167
GO:0043226
GO:0055114
WBGene00001486
cea2.c.13123
Participates
as a component of
2 Iron:FXN [mitochondrial matrix] (Caenorhabditis elegans)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Caenorhabditis elegans)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Caenorhabditis elegans)
Inferred From
FXN(81-210) [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_495183.1
PRO
Q9TY03
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