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OxA-ARSA(19-444) [lysosomal lumen]
Stable Identifier
R-BTA-508497
Type
Protein [EntityWithAccessionedSequence]
Species
Bos taurus
Compartment
lysosomal lumen
Synonyms
Q08DD1
Locations in the PathwayBrowser
Expand all
Metabolism (Bos taurus)
Metabolism of lipids (Bos taurus)
Sphingolipid metabolism (Bos taurus)
Glycosphingolipid metabolism (Bos taurus)
Glycosphingolipid catabolism (Bos taurus)
ARSA removes sulfate from PSAP(195-273):Sulfatide (Bos taurus)
active ARSA:Ca2+ [lysosomal lumen] (Bos taurus)
OxA-ARSA(19-444) [lysosomal lumen] (Bos taurus)
ARSA removes sulfate from SM3 (Bos taurus)
active ARSA:Ca2+ [lysosomal lumen] (Bos taurus)
OxA-ARSA(19-444) [lysosomal lumen] (Bos taurus)
M6PR transports activated ARSA to the lysosome (Bos taurus)
active ARSA:Ca2+ [lysosomal lumen] (Bos taurus)
OxA-ARSA(19-444) [lysosomal lumen] (Bos taurus)
External Reference Information
External Reference
UniProt:Q08DD1
Reference Genes
BioGPS Gene:505514
ENSEMBL:ENSBTAG00000016053
ENSEMBL:ENSBTAG00000016053.5
KEGG Gene (Bos taurus):505514
Monarch:505514
NCBI Gene:505514
Reference Transcript
RefSeq:XM_005207500.3
RefSeq:NM_001075205.1
Other Identifiers
505514
GO:0003824
GO:0004065
GO:0004098
GO:0005509
GO:0005764
GO:0005773
GO:0005783
GO:0006629
GO:0008484
GO:0016787
GO:0043226
GO:0046872
GO:0110165
Participates
as a component of
active ARSA:Ca2+ [lysosomal lumen] (Bos taurus)
Other forms of this molecule
ARSA(19-444) [extracellular region]
ARSA(448-507) [extracellular region]
ARSA(19-444) [azurophil granule lumen]
ARSA(448-507) [azurophil granule lumen]
ARSA(448-507) [lysosomal lumen]
OxA-ARSA(19-444) [endoplasmic reticulum lumen]
ARSA(448-507) [endoplasmic reticulum lumen]
ARSA(19-444) [endoplasmic reticulum lumen]
Inferred From
OxA-ARSA(19-444) [lysosomal lumen]
(Homo sapiens)
Modified Residues
Name
L-3-oxoalanine (Ser) at 69 (in Homo sapiens)
Coordinate
69
PsiMod Name
L-3-oxoalanine (Ser)
PsiMod Definition
A protein modification that effectively converts an L-serine residue to L-oxoalanine.
Cross References
RefSeq
XP_005207557.1
,
NP_001068673.1
IntEnz
3.1.6.8
Ensembl
ENSBTAP00000021364
,
ENSBTAG00000016053
,
ENSBTAT00000021364
VGNC
50217
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