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Ivacaftor [extracellular region]
Stable Identifier
R-ALL-5678956
Type
ChemicalDrug
Compartment
extracellular region
Synonyms
VX-770, Kalydeco
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Disorders of transmembrane transporters (Homo sapiens)
ABC transporter disorders (Homo sapiens)
Defective CFTR causes cystic fibrosis (Homo sapiens)
Ivacaftor binds CFTR G551D (Homo sapiens)
Ivacaftor [extracellular region]
Ivacaftor:CFTR G551D [plasma membrane] (Homo sapiens)
Ivacaftor [extracellular region]
Ivacaftor:CFTR G551D transports Cl- from cytosol to extracellular region (Homo sapiens)
Ivacaftor:CFTR G551D [plasma membrane] (Homo sapiens)
Ivacaftor [extracellular region]
External Reference Information
External Reference
ivacaftor [Guide to Pharmacology:4342]
Participates
as an input of
Ivacaftor binds CFTR G551D (Homo sapiens)
as a component of
Ivacaftor:CFTR G551D [plasma membrane] (Homo sapiens)
Disease
Name
Identifier
Synonyms
cystic fibrosis
DOID:1485
mucoviscidosis, CF
Cross References
ChEBI
66901
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