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L-Ala [mitochondrial matrix]
Stable Identifier
R-ALL-379697
Type
Chemical Compound [SimpleEntity]
Compartment
mitochondrial matrix
Synonyms
L-2-Aminopropionic acid, L-alanine zwitterion, L-alanine, L-alpha-Alanine
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Plasmodium falciparum
Rattus norvegicus
Saccharomyces cerevisiae
Schizosaccharomyces pombe
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of amino acids and derivatives (Bos taurus)
Alanine metabolism (Bos taurus)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Bos taurus)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Bos taurus)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Bos taurus)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Bos taurus)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Bos taurus)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Bos taurus)
L-Ala [mitochondrial matrix]
Metabolism (Caenorhabditis elegans)
Metabolism of amino acids and derivatives (Caenorhabditis elegans)
Alanine metabolism (Caenorhabditis elegans)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Caenorhabditis elegans)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Caenorhabditis elegans)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Caenorhabditis elegans)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Caenorhabditis elegans)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Caenorhabditis elegans)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Caenorhabditis elegans)
L-Ala [mitochondrial matrix]
Metabolism (Canis familiaris)
Metabolism of amino acids and derivatives (Canis familiaris)
Glyoxylate metabolism and glycine degradation (Canis familiaris)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Canis familiaris)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Canis familiaris)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Canis familiaris)
L-Ala [mitochondrial matrix]
Metabolism (Danio rerio)
Metabolism of amino acids and derivatives (Danio rerio)
Alanine metabolism (Danio rerio)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Danio rerio)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Danio rerio)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Danio rerio)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Danio rerio)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Danio rerio)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Danio rerio)
L-Ala [mitochondrial matrix]
Metabolism (Dictyostelium discoideum)
Metabolism of amino acids and derivatives (Dictyostelium discoideum)
Alanine metabolism (Dictyostelium discoideum)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Dictyostelium discoideum)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Dictyostelium discoideum)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Dictyostelium discoideum)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Dictyostelium discoideum)
L-Ala [mitochondrial matrix]
Metabolism (Drosophila melanogaster)
Metabolism of amino acids and derivatives (Drosophila melanogaster)
Alanine metabolism (Drosophila melanogaster)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Drosophila melanogaster)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Drosophila melanogaster)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Drosophila melanogaster)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Drosophila melanogaster)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Drosophila melanogaster)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Drosophila melanogaster)
L-Ala [mitochondrial matrix]
Metabolism (Gallus gallus)
Metabolism of amino acids and derivatives (Gallus gallus)
Alanine metabolism (Gallus gallus)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Gallus gallus)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Gallus gallus)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Gallus gallus)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Gallus gallus)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Gallus gallus)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Gallus gallus)
L-Ala [mitochondrial matrix]
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Alanine metabolism (Homo sapiens)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Homo sapiens)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Homo sapiens)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Homo sapiens)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Homo sapiens)
L-Ala [mitochondrial matrix]
Metabolism of nucleotides (Homo sapiens)
Nucleotide catabolism (Homo sapiens)
Pyrimidine catabolism (Homo sapiens)
(R)-3-aminoisobutyric acid + pyruvate => 2-methyl-3-oxopropanoate + alanine (Homo sapiens)
L-Ala [mitochondrial matrix]
beta-alanine + pyruvate => 3-oxopropanoate + alanine (Homo sapiens)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Homo sapiens)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Homo sapiens)
L-Ala [mitochondrial matrix]
Metabolism of proteins (Homo sapiens)
Translation (Homo sapiens)
tRNA Aminoacylation (Homo sapiens)
Mitochondrial tRNA aminoacylation (Homo sapiens)
alanine + tRNA(Ala) + ATP => Ala-tRNA(Ala) + AMP + pyrophosphate (Homo sapiens)
L-Ala [mitochondrial matrix]
Metabolism (Mus musculus)
Metabolism of amino acids and derivatives (Mus musculus)
Alanine metabolism (Mus musculus)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Mus musculus)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Mus musculus)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Mus musculus)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Mus musculus)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Mus musculus)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Mus musculus)
L-Ala [mitochondrial matrix]
Metabolism (Plasmodium falciparum)
Mitochondrial iron-sulfur cluster biogenesis (Plasmodium falciparum)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Plasmodium falciparum)
L-Ala [mitochondrial matrix]
Metabolism (Rattus norvegicus)
Metabolism of amino acids and derivatives (Rattus norvegicus)
Alanine metabolism (Rattus norvegicus)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Rattus norvegicus)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Rattus norvegicus)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Rattus norvegicus)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Rattus norvegicus)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Rattus norvegicus)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Rattus norvegicus)
L-Ala [mitochondrial matrix]
Metabolism (Saccharomyces cerevisiae)
Metabolism of amino acids and derivatives (Saccharomyces cerevisiae)
Alanine metabolism (Saccharomyces cerevisiae)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Saccharomyces cerevisiae)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Saccharomyces cerevisiae)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Saccharomyces cerevisiae)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Saccharomyces cerevisiae)
L-Ala [mitochondrial matrix]
Metabolism (Schizosaccharomyces pombe)
Metabolism of amino acids and derivatives (Schizosaccharomyces pombe)
Alanine metabolism (Schizosaccharomyces pombe)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Schizosaccharomyces pombe)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Schizosaccharomyces pombe)
L-Ala [mitochondrial matrix]
Metabolism (Sus scrofa)
Metabolism of amino acids and derivatives (Sus scrofa)
Alanine metabolism (Sus scrofa)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Sus scrofa)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Sus scrofa)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Sus scrofa)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Sus scrofa)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Sus scrofa)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Sus scrofa)
L-Ala [mitochondrial matrix]
Metabolism (Xenopus tropicalis)
Metabolism of amino acids and derivatives (Xenopus tropicalis)
Alanine metabolism (Xenopus tropicalis)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Xenopus tropicalis)
L-Ala [mitochondrial matrix]
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Xenopus tropicalis)
L-Ala [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Xenopus tropicalis)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Xenopus tropicalis)
L-Ala [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Xenopus tropicalis)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Xenopus tropicalis)
L-Ala [mitochondrial matrix]
External Reference Information
External Reference
L-alanine zwitterion [ChEBI:57972]
Participates
as an input of
alanine + tRNA(Ala) + ATP => Ala-tRNA(Ala) + AMP + pyrophosphate (Homo sapiens)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Danio rerio)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Homo sapiens)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Mus musculus)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Rattus norvegicus)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Bos taurus)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Sus scrofa)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Xenopus tropicalis)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Gallus gallus)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Drosophila melanogaster)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Caenorhabditis elegans)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Dictyostelium discoideum)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Schizosaccharomyces pombe)
PXLP-K341-GPT2 transaminates L-Ala to form PYR (Saccharomyces cerevisiae)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Danio rerio)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Homo sapiens)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Mus musculus)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Rattus norvegicus)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Canis familiaris)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Bos taurus)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Sus scrofa)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Xenopus tropicalis)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Gallus gallus)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Drosophila melanogaster)
Mitochondrial AGXT2 tetramer transaminates glyoxylate and alanine to glycine and pyruvate (Caenorhabditis elegans)
as an output of
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Plasmodium falciparum)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Saccharomyces cerevisiae)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Dictyostelium discoideum)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Caenorhabditis elegans)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Drosophila melanogaster)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Gallus gallus)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Xenopus tropicalis)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Danio rerio)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Sus scrofa)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Bos taurus)
(R)-3-aminoisobutyric acid + pyruvate => 2-methyl-3-oxopropanoate + alanine (Homo sapiens)
(R)-3-aminoisobutyric acid + pyruvate => 2-methyl-3-oxopropanoate + alanine (Rattus norvegicus)
beta-alanine + pyruvate => 3-oxopropanoate + alanine (Homo sapiens)
beta-alanine + pyruvate => 3-oxopropanoate + alanine (Rattus norvegicus)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Homo sapiens)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Mus musculus)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Rattus norvegicus)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Bos taurus)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Sus scrofa)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Danio rerio)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Xenopus tropicalis)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Gallus gallus)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Drosophila melanogaster)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Caenorhabditis elegans)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Dictyostelium discoideum)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Schizosaccharomyces pombe)
PXLP-K341-GPT2 transaminates PYR to form L-Ala (Saccharomyces cerevisiae)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Homo sapiens)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Mus musculus)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Rattus norvegicus)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Canis familiaris)
Other forms of this molecule
L-Ala [extracellular region]
L-Ala [peroxisomal matrix]
L-Ala [cytosol]
Cross References
COMPOUND
C00041
ZINC
000004658553
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