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GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Stable Identifier
R-ALL-2162223
Type
OtherEntity
Compartment
lysosomal lumen
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Hyaluronan metabolism (Bos taurus)
Hyaluronan uptake and degradation (Bos taurus)
GUSB tetramer hydrolyses (HA)2 (Bos taurus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXA cleaves the terminal GalNAc from small HA fragments (Bos taurus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Bos taurus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Caenorhabditis elegans)
Metabolism of carbohydrates (Caenorhabditis elegans)
Glycosaminoglycan metabolism (Caenorhabditis elegans)
Hyaluronan metabolism (Caenorhabditis elegans)
Hyaluronan uptake and degradation (Caenorhabditis elegans)
GUSB tetramer hydrolyses (HA)2 (Caenorhabditis elegans)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXA cleaves the terminal GalNAc from small HA fragments (Caenorhabditis elegans)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Caenorhabditis elegans)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Hyaluronan metabolism (Canis familiaris)
Hyaluronan uptake and degradation (Canis familiaris)
GUSB tetramer hydrolyses (HA)2 (Canis familiaris)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXA cleaves the terminal GalNAc from small HA fragments (Canis familiaris)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Canis familiaris)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Dictyostelium discoideum)
Metabolism of carbohydrates (Dictyostelium discoideum)
Glycosaminoglycan metabolism (Dictyostelium discoideum)
Hyaluronan metabolism (Dictyostelium discoideum)
Hyaluronan uptake and degradation (Dictyostelium discoideum)
HEXA cleaves the terminal GalNAc from small HA fragments (Dictyostelium discoideum)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Dictyostelium discoideum)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Drosophila melanogaster)
Metabolism of carbohydrates (Drosophila melanogaster)
Glycosaminoglycan metabolism (Drosophila melanogaster)
Hyaluronan metabolism (Drosophila melanogaster)
Hyaluronan uptake and degradation (Drosophila melanogaster)
GUSB tetramer hydrolyses (HA)2 (Drosophila melanogaster)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXA cleaves the terminal GalNAc from small HA fragments (Drosophila melanogaster)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Drosophila melanogaster)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Hyaluronan metabolism (Gallus gallus)
Hyaluronan uptake and degradation (Gallus gallus)
GUSB tetramer hydrolyses (HA)2 (Gallus gallus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXA cleaves the terminal GalNAc from small HA fragments (Gallus gallus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Gallus gallus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with glycosaminoglycan metabolism (Homo sapiens)
Defective HEXA causes GM2G1 (Homo sapiens)
Defective HEXA does not cleave the terminall GalNAc from small HA fragments (Homo sapiens)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Defective HEXB causes GM2G2 (Homo sapiens)
Defective HEXB does not cleave the terminal GalNAc from HA fragments (Homo sapiens)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Hyaluronan metabolism (Homo sapiens)
Hyaluronan uptake and degradation (Homo sapiens)
GUSB tetramer hydrolyses (HA)2 (Homo sapiens)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXA cleaves the terminal GalNAc from small HA fragments (Homo sapiens)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Homo sapiens)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Hyaluronan metabolism (Mus musculus)
Hyaluronan uptake and degradation (Mus musculus)
GUSB tetramer hydrolyses (HA)2 (Mus musculus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXA cleaves the terminal GalNAc from small HA fragments (Mus musculus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Mus musculus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Hyaluronan metabolism (Rattus norvegicus)
Hyaluronan uptake and degradation (Rattus norvegicus)
GUSB tetramer hydrolyses (HA)2 (Rattus norvegicus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXA cleaves the terminal GalNAc from small HA fragments (Rattus norvegicus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Rattus norvegicus)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Hyaluronan metabolism (Sus scrofa)
Hyaluronan uptake and degradation (Sus scrofa)
GUSB tetramer hydrolyses (HA)2 (Sus scrofa)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXA cleaves the terminal GalNAc from small HA fragments (Sus scrofa)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Sus scrofa)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Hyaluronan metabolism (Xenopus tropicalis)
Hyaluronan uptake and degradation (Xenopus tropicalis)
GUSB tetramer hydrolyses (HA)2 (Xenopus tropicalis)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
HEXB cleaves the terminal GalNAc from small HA fragments (Xenopus tropicalis)
GlcNAc-GlcA-GlcNAc [lysosomal lumen]
Participates
as an input of
Defective HEXA does not cleave the terminall GalNAc from small HA fragments (Homo sapiens)
Defective HEXB does not cleave the terminal GalNAc from HA fragments (Homo sapiens)
HEXB cleaves the terminal GalNAc from small HA fragments (Dictyostelium discoideum)
HEXB cleaves the terminal GalNAc from small HA fragments (Caenorhabditis elegans)
HEXB cleaves the terminal GalNAc from small HA fragments (Drosophila melanogaster)
HEXB cleaves the terminal GalNAc from small HA fragments (Gallus gallus)
HEXB cleaves the terminal GalNAc from small HA fragments (Xenopus tropicalis)
HEXB cleaves the terminal GalNAc from small HA fragments (Sus scrofa)
HEXB cleaves the terminal GalNAc from small HA fragments (Bos taurus)
HEXB cleaves the terminal GalNAc from small HA fragments (Canis familiaris)
HEXB cleaves the terminal GalNAc from small HA fragments (Rattus norvegicus)
HEXB cleaves the terminal GalNAc from small HA fragments (Mus musculus)
HEXB cleaves the terminal GalNAc from small HA fragments (Homo sapiens)
HEXA cleaves the terminal GalNAc from small HA fragments (Dictyostelium discoideum)
HEXA cleaves the terminal GalNAc from small HA fragments (Caenorhabditis elegans)
HEXA cleaves the terminal GalNAc from small HA fragments (Drosophila melanogaster)
HEXA cleaves the terminal GalNAc from small HA fragments (Gallus gallus)
HEXA cleaves the terminal GalNAc from small HA fragments (Sus scrofa)
HEXA cleaves the terminal GalNAc from small HA fragments (Bos taurus)
HEXA cleaves the terminal GalNAc from small HA fragments (Canis familiaris)
HEXA cleaves the terminal GalNAc from small HA fragments (Rattus norvegicus)
HEXA cleaves the terminal GalNAc from small HA fragments (Mus musculus)
HEXA cleaves the terminal GalNAc from small HA fragments (Homo sapiens)
as an output of
GUSB tetramer hydrolyses (HA)2 (Caenorhabditis elegans)
GUSB tetramer hydrolyses (HA)2 (Drosophila melanogaster)
GUSB tetramer hydrolyses (HA)2 (Gallus gallus)
GUSB tetramer hydrolyses (HA)2 (Xenopus tropicalis)
GUSB tetramer hydrolyses (HA)2 (Sus scrofa)
GUSB tetramer hydrolyses (HA)2 (Bos taurus)
GUSB tetramer hydrolyses (HA)2 (Canis familiaris)
GUSB tetramer hydrolyses (HA)2 (Rattus norvegicus)
GUSB tetramer hydrolyses (HA)2 (Mus musculus)
GUSB tetramer hydrolyses (HA)2 (Homo sapiens)
Cross References
ChEBI
63563
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