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linker chain(2) [lysosomal lumen]
Stable Identifier
R-ALL-2090075
Type
Chemical Compound [SimpleEntity]
Compartment
lysosomal lumen
Synonyms
Gal-Gal-Xyl- chain, beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Heparan sulfate/heparin (HS-GAG) metabolism (Bos taurus)
HS-GAG degradation (Bos taurus)
GLB1 hydrolyses linker chain(2) (Bos taurus)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Bos taurus)
linker chain(2) [lysosomal lumen]
Metabolism (Caenorhabditis elegans)
Metabolism of carbohydrates (Caenorhabditis elegans)
Glycosaminoglycan metabolism (Caenorhabditis elegans)
Heparan sulfate/heparin (HS-GAG) metabolism (Caenorhabditis elegans)
HS-GAG degradation (Caenorhabditis elegans)
GLB1 hydrolyses linker chain(2) (Caenorhabditis elegans)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Caenorhabditis elegans)
linker chain(2) [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Heparan sulfate/heparin (HS-GAG) metabolism (Canis familiaris)
HS-GAG degradation (Canis familiaris)
GLB1 hydrolyses linker chain(2) (Canis familiaris)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Canis familiaris)
linker chain(2) [lysosomal lumen]
Metabolism (Danio rerio)
Metabolism of carbohydrates (Danio rerio)
Glycosaminoglycan metabolism (Danio rerio)
Heparan sulfate/heparin (HS-GAG) metabolism (Danio rerio)
HS-GAG degradation (Danio rerio)
GLB1 hydrolyses linker chain(2) (Danio rerio)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Danio rerio)
linker chain(2) [lysosomal lumen]
Metabolism (Dictyostelium discoideum)
Metabolism of carbohydrates (Dictyostelium discoideum)
Glycosaminoglycan metabolism (Dictyostelium discoideum)
Heparan sulfate/heparin (HS-GAG) metabolism (Dictyostelium discoideum)
HS-GAG degradation (Dictyostelium discoideum)
GLB1 hydrolyses linker chain(2) (Dictyostelium discoideum)
linker chain(2) [lysosomal lumen]
Metabolism (Drosophila melanogaster)
Metabolism of carbohydrates (Drosophila melanogaster)
Glycosaminoglycan metabolism (Drosophila melanogaster)
Heparan sulfate/heparin (HS-GAG) metabolism (Drosophila melanogaster)
HS-GAG degradation (Drosophila melanogaster)
GLB1 hydrolyses linker chain(2) (Drosophila melanogaster)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Drosophila melanogaster)
linker chain(2) [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Heparan sulfate/heparin (HS-GAG) metabolism (Gallus gallus)
HS-GAG degradation (Gallus gallus)
GLB1 hydrolyses linker chain(2) (Gallus gallus)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Gallus gallus)
linker chain(2) [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of carbohydrate metabolism (Homo sapiens)
Mucopolysaccharidoses (Homo sapiens)
MPS IV - Morquio syndrome B (Homo sapiens)
Defective GLB1 does not hydrolyse linker chain(2) (Homo sapiens)
linker chain(2) [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Heparan sulfate/heparin (HS-GAG) metabolism (Homo sapiens)
HS-GAG degradation (Homo sapiens)
GLB1 hydrolyses linker chain(2) (Homo sapiens)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Homo sapiens)
linker chain(2) [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Heparan sulfate/heparin (HS-GAG) metabolism (Mus musculus)
HS-GAG degradation (Mus musculus)
GLB1 hydrolyses linker chain(2) (Mus musculus)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Mus musculus)
linker chain(2) [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Heparan sulfate/heparin (HS-GAG) metabolism (Rattus norvegicus)
HS-GAG degradation (Rattus norvegicus)
GLB1 hydrolyses linker chain(2) (Rattus norvegicus)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Rattus norvegicus)
linker chain(2) [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Heparan sulfate/heparin (HS-GAG) metabolism (Sus scrofa)
HS-GAG degradation (Sus scrofa)
GLB1 hydrolyses linker chain(2) (Sus scrofa)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Sus scrofa)
linker chain(2) [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Heparan sulfate/heparin (HS-GAG) metabolism (Xenopus tropicalis)
HS-GAG degradation (Xenopus tropicalis)
GLB1 hydrolyses linker chain(2) (Xenopus tropicalis)
linker chain(2) [lysosomal lumen]
GUSB tetramer hydrolyses CS/HS precursor (Xenopus tropicalis)
linker chain(2) [lysosomal lumen]
External Reference Information
External Reference
beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group [ChEBI:63503]
Participates
as an input of
Defective GLB1 does not hydrolyse linker chain(2) (Homo sapiens)
GLB1 hydrolyses linker chain(2) (Dictyostelium discoideum)
GLB1 hydrolyses linker chain(2) (Caenorhabditis elegans)
GLB1 hydrolyses linker chain(2) (Drosophila melanogaster)
GLB1 hydrolyses linker chain(2) (Gallus gallus)
GLB1 hydrolyses linker chain(2) (Xenopus tropicalis)
GLB1 hydrolyses linker chain(2) (Danio rerio)
GLB1 hydrolyses linker chain(2) (Sus scrofa)
GLB1 hydrolyses linker chain(2) (Bos taurus)
GLB1 hydrolyses linker chain(2) (Canis familiaris)
GLB1 hydrolyses linker chain(2) (Rattus norvegicus)
GLB1 hydrolyses linker chain(2) (Mus musculus)
GLB1 hydrolyses linker chain(2) (Homo sapiens)
as an output of
GUSB tetramer hydrolyses CS/HS precursor (Caenorhabditis elegans)
GUSB tetramer hydrolyses CS/HS precursor (Drosophila melanogaster)
GUSB tetramer hydrolyses CS/HS precursor (Gallus gallus)
GUSB tetramer hydrolyses CS/HS precursor (Xenopus tropicalis)
GUSB tetramer hydrolyses CS/HS precursor (Danio rerio)
GUSB tetramer hydrolyses CS/HS precursor (Sus scrofa)
GUSB tetramer hydrolyses CS/HS precursor (Bos taurus)
GUSB tetramer hydrolyses CS/HS precursor (Canis familiaris)
GUSB tetramer hydrolyses CS/HS precursor (Rattus norvegicus)
GUSB tetramer hydrolyses CS/HS precursor (Mus musculus)
GUSB tetramer hydrolyses CS/HS precursor (Homo sapiens)
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