Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Editorial Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Content
Table of Contents
DOIs
Data Schema
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Computationally inferred events
Linking to Us
Citing us
Tools
Pathway Browser
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Overlays
DisGeNET
Web
API
Advanced Data Search
Site Search
Community
Icon Library
Outreach
Events
Training
Publications
Partners
Papers Citing Us
Resources Guide
Collaboration
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Editorial Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Content
Table of Contents
DOIs
Data Schema
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Computationally inferred events
Linking to Us
Citing us
Tools
Pathway Browser
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Overlays
DisGeNET
Web
API
Advanced Data Search
Site Search
Community
Icon Library
Outreach
Events
Training
Publications
Partners
Papers Citing Us
Resources Guide
Collaboration
Download
Search ...
Go!
ChEBI:63516 chain [lysosomal lumen]
Stable Identifier
R-ALL-2065269
Type
Chemical Compound [SimpleEntity]
Compartment
lysosomal lumen
Synonyms
beta-D-GalNAc-(1->4)-beta-D-IdoA-(1->3)-beta-D-GalNAc4S-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Chondroitin sulfate/dermatan sulfate metabolism (Bos taurus)
CS/DS degradation (Bos taurus)
HEXA cleaves the terminal GalNAc from DS (Bos taurus)
ChEBI:63516 chain [lysosomal lumen]
HEXB cleaves the terminal GalNAc from DS (Bos taurus)
ChEBI:63516 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Bos taurus)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Caenorhabditis elegans)
Metabolism of carbohydrates (Caenorhabditis elegans)
Glycosaminoglycan metabolism (Caenorhabditis elegans)
Chondroitin sulfate/dermatan sulfate metabolism (Caenorhabditis elegans)
CS/DS degradation (Caenorhabditis elegans)
HEXA cleaves the terminal GalNAc from DS (Caenorhabditis elegans)
ChEBI:63516 chain [lysosomal lumen]
HEXB cleaves the terminal GalNAc from DS (Caenorhabditis elegans)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Chondroitin sulfate/dermatan sulfate metabolism (Canis familiaris)
CS/DS degradation (Canis familiaris)
HEXA cleaves the terminal GalNAc from DS (Canis familiaris)
ChEBI:63516 chain [lysosomal lumen]
HEXB cleaves the terminal GalNAc from DS (Canis familiaris)
ChEBI:63516 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Canis familiaris)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Danio rerio)
Metabolism of carbohydrates (Danio rerio)
Glycosaminoglycan metabolism (Danio rerio)
Chondroitin sulfate/dermatan sulfate metabolism (Danio rerio)
CS/DS degradation (Danio rerio)
HEXA cleaves the terminal GalNAc from DS (Danio rerio)
ChEBI:63516 chain [lysosomal lumen]
HEXB cleaves the terminal GalNAc from DS (Danio rerio)
ChEBI:63516 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Danio rerio)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Dictyostelium discoideum)
Metabolism of carbohydrates (Dictyostelium discoideum)
Glycosaminoglycan metabolism (Dictyostelium discoideum)
Chondroitin sulfate/dermatan sulfate metabolism (Dictyostelium discoideum)
CS/DS degradation (Dictyostelium discoideum)
HEXA cleaves the terminal GalNAc from DS (Dictyostelium discoideum)
ChEBI:63516 chain [lysosomal lumen]
HEXB cleaves the terminal GalNAc from DS (Dictyostelium discoideum)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Drosophila melanogaster)
Metabolism of carbohydrates (Drosophila melanogaster)
Glycosaminoglycan metabolism (Drosophila melanogaster)
Chondroitin sulfate/dermatan sulfate metabolism (Drosophila melanogaster)
CS/DS degradation (Drosophila melanogaster)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Drosophila melanogaster)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Chondroitin sulfate/dermatan sulfate metabolism (Gallus gallus)
CS/DS degradation (Gallus gallus)
HEXA cleaves the terminal GalNAc from DS (Gallus gallus)
ChEBI:63516 chain [lysosomal lumen]
HEXB cleaves the terminal GalNAc from DS (Gallus gallus)
ChEBI:63516 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Gallus gallus)
ChEBI:63516 chain [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with glycosaminoglycan metabolism (Homo sapiens)
Defective HEXA causes GM2G1 (Homo sapiens)
Defective HEXA does not cleave the terminal GalNAc from DS (Homo sapiens)
ChEBI:63516 chain [lysosomal lumen]
Defective HEXB causes GM2G2 (Homo sapiens)
Defective HEXB does not cleave the terminal GalNAc from DS (Homo sapiens)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
CS/DS degradation (Homo sapiens)
HEXA cleaves the terminal GalNAc from DS (Homo sapiens)
ChEBI:63516 chain [lysosomal lumen]
HEXB cleaves the terminal GalNAc from DS (Homo sapiens)
ChEBI:63516 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Homo sapiens)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Chondroitin sulfate/dermatan sulfate metabolism (Mus musculus)
CS/DS degradation (Mus musculus)
HEXA cleaves the terminal GalNAc from DS (Mus musculus)
ChEBI:63516 chain [lysosomal lumen]
HEXB cleaves the terminal GalNAc from DS (Mus musculus)
ChEBI:63516 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Mus musculus)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Chondroitin sulfate/dermatan sulfate metabolism (Rattus norvegicus)
CS/DS degradation (Rattus norvegicus)
HEXA cleaves the terminal GalNAc from DS (Rattus norvegicus)
ChEBI:63516 chain [lysosomal lumen]
HEXB cleaves the terminal GalNAc from DS (Rattus norvegicus)
ChEBI:63516 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Rattus norvegicus)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Chondroitin sulfate/dermatan sulfate metabolism (Sus scrofa)
CS/DS degradation (Sus scrofa)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Sus scrofa)
ChEBI:63516 chain [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Chondroitin sulfate/dermatan sulfate metabolism (Xenopus tropicalis)
CS/DS degradation (Xenopus tropicalis)
HEXB cleaves the terminal GalNAc from DS (Xenopus tropicalis)
ChEBI:63516 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Xenopus tropicalis)
ChEBI:63516 chain [lysosomal lumen]
External Reference Information
External Reference
beta-D-GalNAc-(1->4)-beta-D-IdoA-(1->3)-beta-D-GalNAc4S-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group [ChEBI:63516]
Participant Of
input
Defective HEXA does not cleave the terminal GalNAc from DS
Defective HEXB does not cleave the terminal GalNAc from DS
HEXA cleaves the terminal GalNAc from DS
HEXA cleaves the terminal GalNAc from DS
HEXA cleaves the terminal GalNAc from DS
HEXA cleaves the terminal GalNAc from DS
HEXA cleaves the terminal GalNAc from DS
HEXA cleaves the terminal GalNAc from DS
HEXA cleaves the terminal GalNAc from DS
HEXA cleaves the terminal GalNAc from DS
HEXA cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
HEXB cleaves the terminal GalNAc from DS
output
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain)
© 2021
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text