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ChEBI:63517 chain [lysosomal lumen]
Stable Identifier
R-ALL-2065213
Type
Chemical Compound [SimpleEntity]
Compartment
lysosomal lumen
Synonyms
beta-D-GalNAc-(1->4)-beta-D-IdoA2S-(1->3)-beta-D-GalNAc4S-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Canis familiaris
Danio rerio
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Chondroitin sulfate/dermatan sulfate metabolism (Bos taurus)
CS/DS degradation (Bos taurus)
ARSB hydrolyses DS (Bos taurus)
ChEBI:63517 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Bos taurus)
ChEBI:63517 chain [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Chondroitin sulfate/dermatan sulfate metabolism (Canis familiaris)
CS/DS degradation (Canis familiaris)
ARSB hydrolyses DS (Canis familiaris)
ChEBI:63517 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Canis familiaris)
ChEBI:63517 chain [lysosomal lumen]
Metabolism (Danio rerio)
Metabolism of carbohydrates (Danio rerio)
Glycosaminoglycan metabolism (Danio rerio)
Chondroitin sulfate/dermatan sulfate metabolism (Danio rerio)
CS/DS degradation (Danio rerio)
ARSB hydrolyses DS (Danio rerio)
ChEBI:63517 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Danio rerio)
ChEBI:63517 chain [lysosomal lumen]
Metabolism (Drosophila melanogaster)
Metabolism of carbohydrates (Drosophila melanogaster)
Glycosaminoglycan metabolism (Drosophila melanogaster)
Chondroitin sulfate/dermatan sulfate metabolism (Drosophila melanogaster)
CS/DS degradation (Drosophila melanogaster)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Drosophila melanogaster)
ChEBI:63517 chain [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Chondroitin sulfate/dermatan sulfate metabolism (Gallus gallus)
CS/DS degradation (Gallus gallus)
ARSB hydrolyses DS (Gallus gallus)
ChEBI:63517 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Gallus gallus)
ChEBI:63517 chain [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of carbohydrate metabolism (Homo sapiens)
Mucopolysaccharidoses (Homo sapiens)
MPS II - Hunter syndrome (Homo sapiens)
Defective IDS does not hydrolyse dermatan sulfate (Chebi:63517 chain) (Homo sapiens)
ChEBI:63517 chain [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
CS/DS degradation (Homo sapiens)
ARSB hydrolyses DS (Homo sapiens)
ChEBI:63517 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Homo sapiens)
ChEBI:63517 chain [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Chondroitin sulfate/dermatan sulfate metabolism (Mus musculus)
CS/DS degradation (Mus musculus)
ARSB hydrolyses DS (Mus musculus)
ChEBI:63517 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Mus musculus)
ChEBI:63517 chain [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Chondroitin sulfate/dermatan sulfate metabolism (Rattus norvegicus)
CS/DS degradation (Rattus norvegicus)
ARSB hydrolyses DS (Rattus norvegicus)
ChEBI:63517 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Rattus norvegicus)
ChEBI:63517 chain [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Chondroitin sulfate/dermatan sulfate metabolism (Sus scrofa)
CS/DS degradation (Sus scrofa)
ARSB hydrolyses DS (Sus scrofa)
ChEBI:63517 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Sus scrofa)
ChEBI:63517 chain [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Chondroitin sulfate/dermatan sulfate metabolism (Xenopus tropicalis)
CS/DS degradation (Xenopus tropicalis)
ARSB hydrolyses DS (Xenopus tropicalis)
ChEBI:63517 chain [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Xenopus tropicalis)
ChEBI:63517 chain [lysosomal lumen]
External Reference Information
External Reference
beta-D-GalNAc-(1->4)-beta-D-IdoA2S-(1->3)-beta-D-GalNAc4S-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group [ChEBI:63517]
Participates
as an input of
Defective IDS does not hydrolyse dermatan sulfate (Chebi:63517 chain) (Homo sapiens)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Drosophila melanogaster)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Gallus gallus)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Xenopus tropicalis)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Danio rerio)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Sus scrofa)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Bos taurus)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Canis familiaris)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Rattus norvegicus)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Mus musculus)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Homo sapiens)
as an output of
ARSB hydrolyses DS (Gallus gallus)
ARSB hydrolyses DS (Xenopus tropicalis)
ARSB hydrolyses DS (Danio rerio)
ARSB hydrolyses DS (Sus scrofa)
ARSB hydrolyses DS (Bos taurus)
ARSB hydrolyses DS (Canis familiaris)
ARSB hydrolyses DS (Rattus norvegicus)
ARSB hydrolyses DS (Mus musculus)
ARSB hydrolyses DS (Homo sapiens)
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