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Ca2+ [lysosomal lumen]
Stable Identifier
R-ALL-1606834
Type
Chemical Compound [SimpleEntity]
Compartment
lysosomal lumen
Synonyms
Calcium, calcium(2+)
Icon
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Canis familiaris
Danio rerio
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Chondroitin sulfate/dermatan sulfate metabolism (Bos taurus)
CS/DS degradation (Bos taurus)
ARSB hydrolyses C4S/C6S chains (Bos taurus)
ARSB:Ca2+ [lysosomal lumen] (Bos taurus)
Ca2+ [lysosomal lumen]
ARSB hydrolyses DS (Bos taurus)
ARSB:Ca2+ [lysosomal lumen] (Bos taurus)
Ca2+ [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Bos taurus)
IDS dimer [lysosomal lumen] (Bos taurus)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Bos taurus)
HS-GAG degradation (Bos taurus)
IDS hydrolyses Heparan sulfate chain(5) (Bos taurus)
IDS dimer [lysosomal lumen] (Bos taurus)
Ca2+ [lysosomal lumen]
Metabolism of lipids (Bos taurus)
Sphingolipid metabolism (Bos taurus)
Glycosphingolipid metabolism (Bos taurus)
Active ARSA translocates to the lysosome (Bos taurus)
active ARSA:Ca2+ [lysosomal lumen] (Bos taurus)
Ca2+ [lysosomal lumen]
Arylsulfatase A hydrolyses sulfate from sulfatide to form cerebroside (Bos taurus)
active ARSA:Ca2+ [lysosomal lumen] (Bos taurus)
Ca2+ [lysosomal lumen]
Transport of small molecules (Bos taurus)
Ion channel transport (Bos taurus)
Stimuli-sensing channels (Bos taurus)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Bos taurus)
Ca2+ [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Chondroitin sulfate/dermatan sulfate metabolism (Canis familiaris)
CS/DS degradation (Canis familiaris)
ARSB hydrolyses C4S/C6S chains (Canis familiaris)
ARSB:Ca2+ [lysosomal lumen] (Canis familiaris)
Ca2+ [lysosomal lumen]
ARSB hydrolyses DS (Canis familiaris)
ARSB:Ca2+ [lysosomal lumen] (Canis familiaris)
Ca2+ [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Canis familiaris)
IDS dimer [lysosomal lumen] (Canis familiaris)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Canis familiaris)
HS-GAG degradation (Canis familiaris)
IDS hydrolyses Heparan sulfate chain(5) (Canis familiaris)
IDS dimer [lysosomal lumen] (Canis familiaris)
Ca2+ [lysosomal lumen]
Metabolism of lipids (Canis familiaris)
Sphingolipid metabolism (Canis familiaris)
Glycosphingolipid metabolism (Canis familiaris)
Active ARSA translocates to the lysosome (Canis familiaris)
active ARSA:Ca2+ [lysosomal lumen] (Canis familiaris)
Ca2+ [lysosomal lumen]
Arylsulfatase A hydrolyses sulfate from sulfatide to form cerebroside (Canis familiaris)
active ARSA:Ca2+ [lysosomal lumen] (Canis familiaris)
Ca2+ [lysosomal lumen]
Transport of small molecules (Canis familiaris)
Ion channel transport (Canis familiaris)
Stimuli-sensing channels (Canis familiaris)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Canis familiaris)
Ca2+ [lysosomal lumen]
Metabolism (Danio rerio)
Metabolism of carbohydrates (Danio rerio)
Glycosaminoglycan metabolism (Danio rerio)
Chondroitin sulfate/dermatan sulfate metabolism (Danio rerio)
CS/DS degradation (Danio rerio)
ARSB hydrolyses C4S/C6S chains (Danio rerio)
ARSB:Ca2+ [lysosomal lumen] (Danio rerio)
Ca2+ [lysosomal lumen]
ARSB hydrolyses DS (Danio rerio)
ARSB:Ca2+ [lysosomal lumen] (Danio rerio)
Ca2+ [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Danio rerio)
IDS dimer [lysosomal lumen] (Danio rerio)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Danio rerio)
HS-GAG degradation (Danio rerio)
IDS hydrolyses Heparan sulfate chain(5) (Danio rerio)
IDS dimer [lysosomal lumen] (Danio rerio)
Ca2+ [lysosomal lumen]
Metabolism of lipids (Danio rerio)
Sphingolipid metabolism (Danio rerio)
Glycosphingolipid metabolism (Danio rerio)
Active ARSA translocates to the lysosome (Danio rerio)
active ARSA:Ca2+ [lysosomal lumen] (Danio rerio)
Ca2+ [lysosomal lumen]
Arylsulfatase A hydrolyses sulfate from sulfatide to form cerebroside (Danio rerio)
active ARSA:Ca2+ [lysosomal lumen] (Danio rerio)
Ca2+ [lysosomal lumen]
Transport of small molecules (Danio rerio)
Ion channel transport (Danio rerio)
Stimuli-sensing channels (Danio rerio)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Danio rerio)
Ca2+ [lysosomal lumen]
Metabolism (Drosophila melanogaster)
Metabolism of carbohydrates (Drosophila melanogaster)
Glycosaminoglycan metabolism (Drosophila melanogaster)
Chondroitin sulfate/dermatan sulfate metabolism (Drosophila melanogaster)
CS/DS degradation (Drosophila melanogaster)
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Drosophila melanogaster)
IDS dimer [lysosomal lumen] (Drosophila melanogaster)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Drosophila melanogaster)
HS-GAG degradation (Drosophila melanogaster)
IDS hydrolyses Heparan sulfate chain(5) (Drosophila melanogaster)
IDS dimer [lysosomal lumen] (Drosophila melanogaster)
Ca2+ [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Chondroitin sulfate/dermatan sulfate metabolism (Gallus gallus)
CS/DS degradation (Gallus gallus)
ARSB hydrolyses C4S/C6S chains (Gallus gallus)
ARSB:Ca2+ [lysosomal lumen] (Gallus gallus)
Ca2+ [lysosomal lumen]
ARSB hydrolyses DS (Gallus gallus)
ARSB:Ca2+ [lysosomal lumen] (Gallus gallus)
Ca2+ [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Gallus gallus)
IDS dimer [lysosomal lumen] (Gallus gallus)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Gallus gallus)
HS-GAG degradation (Gallus gallus)
IDS hydrolyses Heparan sulfate chain(5) (Gallus gallus)
IDS dimer [lysosomal lumen] (Gallus gallus)
Ca2+ [lysosomal lumen]
Metabolism of lipids (Gallus gallus)
Sphingolipid metabolism (Gallus gallus)
Glycosphingolipid metabolism (Gallus gallus)
Active ARSA translocates to the lysosome (Gallus gallus)
active ARSA:Ca2+ [lysosomal lumen] (Gallus gallus)
Ca2+ [lysosomal lumen]
Arylsulfatase A hydrolyses sulfate from sulfatide to form cerebroside (Gallus gallus)
active ARSA:Ca2+ [lysosomal lumen] (Gallus gallus)
Ca2+ [lysosomal lumen]
Transport of small molecules (Gallus gallus)
Ion channel transport (Gallus gallus)
Stimuli-sensing channels (Gallus gallus)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Gallus gallus)
Ca2+ [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of carbohydrate metabolism (Homo sapiens)
Mucopolysaccharidoses (Homo sapiens)
MPS II - Hunter syndrome (Homo sapiens)
Defective IDS does not hydrolyse Heparan sulfate chain(5) (Homo sapiens)
Ca2+:Ca2+:IDS mutants:IDS mutants [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
Defective IDS does not hydrolyse dermatan sulfate (Chebi:63517 chain) (Homo sapiens)
Ca2+:Ca2+:IDS mutants:IDS mutants [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
MPS VI - Maroteaux-Lamy syndrome (Homo sapiens)
Defective ARSB does not hydrolyse C4S/C6S chains (Homo sapiens)
ARSB mutants:Ca2+ [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
Defective ARSB does not hydrolyse DS (Homo sapiens)
ARSB mutants:Ca2+ [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
CS/DS degradation (Homo sapiens)
ARSB hydrolyses C4S/C6S chains (Homo sapiens)
ARSB:Ca2+ [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
ARSB hydrolyses DS (Homo sapiens)
ARSB:Ca2+ [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Homo sapiens)
IDS dimer [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Homo sapiens)
HS-GAG degradation (Homo sapiens)
IDS hydrolyses Heparan sulfate chain(5) (Homo sapiens)
IDS dimer [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
Metabolism of lipids (Homo sapiens)
Sphingolipid metabolism (Homo sapiens)
Glycosphingolipid metabolism (Homo sapiens)
Active ARSA translocates to the lysosome (Homo sapiens)
active ARSA:Ca2+ [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
Arylsulfatase A hydrolyses sulfate from sulfatide to form cerebroside (Homo sapiens)
active ARSA:Ca2+ [lysosomal lumen] (Homo sapiens)
Ca2+ [lysosomal lumen]
Transport of small molecules (Homo sapiens)
Ion channel transport (Homo sapiens)
Stimuli-sensing channels (Homo sapiens)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Homo sapiens)
Ca2+ [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Chondroitin sulfate/dermatan sulfate metabolism (Mus musculus)
CS/DS degradation (Mus musculus)
ARSB hydrolyses C4S/C6S chains (Mus musculus)
ARSB:Ca2+ [lysosomal lumen] (Mus musculus)
Ca2+ [lysosomal lumen]
ARSB hydrolyses DS (Mus musculus)
ARSB:Ca2+ [lysosomal lumen] (Mus musculus)
Ca2+ [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Mus musculus)
IDS dimer [lysosomal lumen] (Mus musculus)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Mus musculus)
HS-GAG degradation (Mus musculus)
IDS hydrolyses Heparan sulfate chain(5) (Mus musculus)
IDS dimer [lysosomal lumen] (Mus musculus)
Ca2+ [lysosomal lumen]
Metabolism of lipids (Mus musculus)
Sphingolipid metabolism (Mus musculus)
Glycosphingolipid metabolism (Mus musculus)
Active ARSA translocates to the lysosome (Mus musculus)
active ARSA:Ca2+ [lysosomal lumen] (Mus musculus)
Ca2+ [lysosomal lumen]
Arylsulfatase A hydrolyses sulfate from sulfatide to form cerebroside (Mus musculus)
active ARSA:Ca2+ [lysosomal lumen] (Mus musculus)
Ca2+ [lysosomal lumen]
Transport of small molecules (Mus musculus)
Ion channel transport (Mus musculus)
Stimuli-sensing channels (Mus musculus)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Mus musculus)
Ca2+ [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Chondroitin sulfate/dermatan sulfate metabolism (Rattus norvegicus)
CS/DS degradation (Rattus norvegicus)
ARSB hydrolyses C4S/C6S chains (Rattus norvegicus)
ARSB:Ca2+ [lysosomal lumen] (Rattus norvegicus)
Ca2+ [lysosomal lumen]
ARSB hydrolyses DS (Rattus norvegicus)
ARSB:Ca2+ [lysosomal lumen] (Rattus norvegicus)
Ca2+ [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Rattus norvegicus)
IDS dimer [lysosomal lumen] (Rattus norvegicus)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Rattus norvegicus)
HS-GAG degradation (Rattus norvegicus)
IDS hydrolyses Heparan sulfate chain(5) (Rattus norvegicus)
IDS dimer [lysosomal lumen] (Rattus norvegicus)
Ca2+ [lysosomal lumen]
Metabolism of lipids (Rattus norvegicus)
Sphingolipid metabolism (Rattus norvegicus)
Glycosphingolipid metabolism (Rattus norvegicus)
Active ARSA translocates to the lysosome (Rattus norvegicus)
active ARSA:Ca2+ [lysosomal lumen] (Rattus norvegicus)
Ca2+ [lysosomal lumen]
Arylsulfatase A hydrolyses sulfate from sulfatide to form cerebroside (Rattus norvegicus)
active ARSA:Ca2+ [lysosomal lumen] (Rattus norvegicus)
Ca2+ [lysosomal lumen]
Transport of small molecules (Rattus norvegicus)
Ion channel transport (Rattus norvegicus)
Stimuli-sensing channels (Rattus norvegicus)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Rattus norvegicus)
Ca2+ [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Chondroitin sulfate/dermatan sulfate metabolism (Sus scrofa)
CS/DS degradation (Sus scrofa)
ARSB hydrolyses C4S/C6S chains (Sus scrofa)
ARSB:Ca2+ [lysosomal lumen] (Sus scrofa)
Ca2+ [lysosomal lumen]
ARSB hydrolyses DS (Sus scrofa)
ARSB:Ca2+ [lysosomal lumen] (Sus scrofa)
Ca2+ [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Sus scrofa)
IDS dimer [lysosomal lumen] (Sus scrofa)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Sus scrofa)
HS-GAG degradation (Sus scrofa)
IDS hydrolyses Heparan sulfate chain(5) (Sus scrofa)
IDS dimer [lysosomal lumen] (Sus scrofa)
Ca2+ [lysosomal lumen]
Metabolism of lipids (Sus scrofa)
Sphingolipid metabolism (Sus scrofa)
Glycosphingolipid metabolism (Sus scrofa)
Active ARSA translocates to the lysosome (Sus scrofa)
active ARSA:Ca2+ [lysosomal lumen] (Sus scrofa)
Ca2+ [lysosomal lumen]
Arylsulfatase A hydrolyses sulfate from sulfatide to form cerebroside (Sus scrofa)
active ARSA:Ca2+ [lysosomal lumen] (Sus scrofa)
Ca2+ [lysosomal lumen]
Transport of small molecules (Sus scrofa)
Ion channel transport (Sus scrofa)
Stimuli-sensing channels (Sus scrofa)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Sus scrofa)
Ca2+ [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Chondroitin sulfate/dermatan sulfate metabolism (Xenopus tropicalis)
CS/DS degradation (Xenopus tropicalis)
ARSB hydrolyses C4S/C6S chains (Xenopus tropicalis)
ARSB:Ca2+ [lysosomal lumen] (Xenopus tropicalis)
Ca2+ [lysosomal lumen]
ARSB hydrolyses DS (Xenopus tropicalis)
ARSB:Ca2+ [lysosomal lumen] (Xenopus tropicalis)
Ca2+ [lysosomal lumen]
IDS hydrolyses dermatan sulfate (Chebi:63517 chain) (Xenopus tropicalis)
IDS dimer [lysosomal lumen] (Xenopus tropicalis)
Ca2+ [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Xenopus tropicalis)
HS-GAG degradation (Xenopus tropicalis)
IDS hydrolyses Heparan sulfate chain(5) (Xenopus tropicalis)
IDS dimer [lysosomal lumen] (Xenopus tropicalis)
Ca2+ [lysosomal lumen]
Metabolism of lipids (Xenopus tropicalis)
Sphingolipid metabolism (Xenopus tropicalis)
Glycosphingolipid metabolism (Xenopus tropicalis)
Active ARSA translocates to the lysosome (Xenopus tropicalis)
active ARSA:Ca2+ [lysosomal lumen] (Xenopus tropicalis)
Ca2+ [lysosomal lumen]
Arylsulfatase A hydrolyses sulfate from sulfatide to form cerebroside (Xenopus tropicalis)
active ARSA:Ca2+ [lysosomal lumen] (Xenopus tropicalis)
Ca2+ [lysosomal lumen]
Transport of small molecules (Xenopus tropicalis)
Ion channel transport (Xenopus tropicalis)
Stimuli-sensing channels (Xenopus tropicalis)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Xenopus tropicalis)
Ca2+ [lysosomal lumen]
External Reference Information
External Reference
calcium(2+) [ChEBI:29108]
Participates
as a component of
ARSB mutants:Ca2+ [lysosomal lumen] (Homo sapiens)
Ca2+:Ca2+:IDS mutants:IDS mutants [lysosomal lumen] (Homo sapiens)
active ARSA:Ca2+ [lysosomal lumen] (Danio rerio)
active ARSA:Ca2+ [lysosomal lumen] (Gallus gallus)
active ARSA:Ca2+ [lysosomal lumen] (Mus musculus)
active ARSA:Ca2+ [lysosomal lumen] (Sus scrofa)
active ARSA:Ca2+ [lysosomal lumen] (Canis familiaris)
active ARSA:Ca2+ [lysosomal lumen] (Rattus norvegicus)
active ARSA:Ca2+ [lysosomal lumen] (Bos taurus)
active ARSA:Ca2+ [lysosomal lumen] (Xenopus tropicalis)
active ARSA:Ca2+ [lysosomal lumen] (Homo sapiens)
ARSB:Ca2+ [lysosomal lumen] (Gallus gallus)
ARSB:Ca2+ [lysosomal lumen] (Canis familiaris)
ARSB:Ca2+ [lysosomal lumen] (Rattus norvegicus)
ARSB:Ca2+ [lysosomal lumen] (Bos taurus)
ARSB:Ca2+ [lysosomal lumen] (Danio rerio)
ARSB:Ca2+ [lysosomal lumen] (Xenopus tropicalis)
ARSB:Ca2+ [lysosomal lumen] (Mus musculus)
ARSB:Ca2+ [lysosomal lumen] (Sus scrofa)
ARSB:Ca2+ [lysosomal lumen] (Homo sapiens)
IDS dimer [lysosomal lumen] (Drosophila melanogaster)
IDS dimer [lysosomal lumen] (Bos taurus)
IDS dimer [lysosomal lumen] (Canis familiaris)
IDS dimer [lysosomal lumen] (Xenopus tropicalis)
IDS dimer [lysosomal lumen] (Danio rerio)
IDS dimer [lysosomal lumen] (Rattus norvegicus)
IDS dimer [lysosomal lumen] (Mus musculus)
IDS dimer [lysosomal lumen] (Gallus gallus)
IDS dimer [lysosomal lumen] (Sus scrofa)
IDS dimer [lysosomal lumen] (Homo sapiens)
as an input of
TPCN1/2 transport lysosomal Ca2+ to cytosol (Gallus gallus)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Xenopus tropicalis)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Danio rerio)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Sus scrofa)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Bos taurus)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Canis familiaris)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Rattus norvegicus)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Mus musculus)
TPCN1/2 transport lysosomal Ca2+ to cytosol (Homo sapiens)
Other forms of this molecule
Ca2+ [platelet dense granule lumen]
Ca2+ [endosome membrane]
Ca2+ [sarcoplasmic reticulum lumen]
Ca2+ [mitochondrial intermembrane space]
Ca2+ [mitochondrial matrix]
Ca2+ [endocytic vesicle lumen]
Ca2+ [endoplasmic reticulum-Golgi intermediate compartment]
Ca2+ [Golgi lumen]
Ca2+ [platelet dense tubular network lumen]
Ca2+ [platelet dense tubular network membrane]
Ca2+ [plasma membrane]
Ca2+ [secretory granule lumen]
Ca2+ [nuclear envelope]
Ca2+ [nucleoplasm]
Ca2+ [mitochondrial inner membrane]
Ca2+ [endoplasmic reticulum membrane]
Ca2+ [endoplasmic reticulum lumen]
Ca2+ [cytosol]
Ca2+ [extracellular region]
Cross References
COMPOUND
C00076
PubChem Substance
8145461
HMDB Metabolite
HMDB0000464
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