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Schema
>
FailedReaction
>
Entries
Defective AHCY does not hydrolyse AdoHcy
Show undefined attributes
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authored
[InstanceEdit:5579090] Jassal, Bijay, 2014-06-06
catalystActivity
[CatalystActivity:9638059] adenosylhomocysteinase activity of AHCY mutants:NAD+ tetramer [cytosol]
category
transition
compartment
[Compartment:70101] cytosol
created
[InstanceEdit:5579090] Jassal, Bijay, 2014-06-06
dbId
5579084
disease
[Disease:5579115] hypermethioninemia
displayName
Defective AHCY does not hydrolyse AdoHcy
edited
[InstanceEdit:5579090] Jassal, Bijay, 2014-06-06
entityFunctionalStatus
[EntityFunctionalStatus:5579113] loss_of_function of AHCY mutants:NAD+ tetramer [cytosol]
eventOf
[Pathway:R-HSA-5578997] Defective AHCY causes HMAHCHD - Homo sapiens
input
[SimpleEntity:R-ALL-71285] AdoHcy [cytosol]
[SimpleEntity:R-ALL-29356] H2O [cytosol]
isChimeric
false
isInDisease
true
isInferred
false
literatureReference
[LiteratureReference:5579036] Catalytic strategy of S-adenosyl-L-homocysteine hydrolase: transition-state stabilization and the avoidance of abortive reactions
[LiteratureReference:5579074] Structure determination of selenomethionyl S-adenosylhomocysteine hydrolase using data at a single wavelength
[LiteratureReference:5579078] S-adenosylhomocysteine hydrolase deficiency in a human: a genetic disorder of methionine metabolism
modified
[InstanceEdit:9830342] Matthews, Lisa, 2023-03-08
name
Defective AHCY does not hydrolyse AdoHcy
normalReaction
[Reaction:R-HSA-174401] AHCY:NAD+ tetramer hydrolyses AdoHcy
releaseDate
2014-12-11
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:5634119] Nakaki, Toshio, 2014-11-03
schemaClass
FailedReaction
species
[Species:48887] Homo sapiens
stId
R-HSA-5579084
summation
[Summation:5579071] Adenosylhomocysteinase (AHCY) is a tetrameric, NAD+-bound, c...
systematicName
AHCY mutants do not hydrolyse AdoHcy
Referrals
(hasEvent)
[Pathway:R-HSA-5578997] Defective AHCY causes HMAHCHD
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