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Hexb [lysosomal lumen]
Stable Identifier
R-RNO-1605605
Type
Protein [EntityWithAccessionedSequence]
Species
Rattus norvegicus
Compartment
lysosomal lumen
Synonyms
HEXB(316-556), Q6AXR4
Locations in the PathwayBrowser
Expand all
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Chondroitin sulfate/dermatan sulfate metabolism (Rattus norvegicus)
CS/DS degradation (Rattus norvegicus)
HEXA cleaves the terminal GalNAc from DS (Rattus norvegicus)
bHEXA [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
HEXB cleaves the terminal GalNAc from DS (Rattus norvegicus)
bHEXB [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
Hyaluronan metabolism (Rattus norvegicus)
Hyaluronan uptake and degradation (Rattus norvegicus)
HEXA cleaves the terminal GalNAc from small HA fragments (Rattus norvegicus)
bHEXA [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
HEXB cleaves the terminal GalNAc from small HA fragments (Rattus norvegicus)
bHEXB [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
Keratan sulfate/keratin metabolism (Rattus norvegicus)
Keratan sulfate degradation (Rattus norvegicus)
HEXA cleaves the terminal GalNAc from keratan sulfate (Rattus norvegicus)
bHEXA [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
HEXB cleaves the terminal GalNAc from keratan sulfate (Rattus norvegicus)
bHEXB [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
Metabolism of lipids (Rattus norvegicus)
Sphingolipid metabolism (Rattus norvegicus)
Glycosphingolipid metabolism (Rattus norvegicus)
Glycosphingolipid catabolism (Rattus norvegicus)
bHEXA hydrolyzes GM2A:GM2 to GM2A:GM3 (Rattus norvegicus)
bHEXA [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
bHEXA,bHEXB hydrolyze GM2A:GA2 to GM2A:LacCer (Rattus norvegicus)
bHEXA,bHEXB [lysosomal lumen] (Rattus norvegicus)
bHEXA [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
bHEXB [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
bHEXA,bHEXB hydrolyze PSAP(195-273):Gb4Cer:PE (Rattus norvegicus)
bHEXA,bHEXB [lysosomal lumen] (Rattus norvegicus)
bHEXA [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
bHEXB [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
bHEXA,bHEXS hydrolyze GM2A:SM2 (Rattus norvegicus)
bHEXA,bHEXS [lysosomal lumen] (Rattus norvegicus)
bHEXA [lysosomal lumen] (Rattus norvegicus)
HEXB dimer [lysosomal lumen] (Rattus norvegicus)
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Hexb [lysosomal lumen] (Rattus norvegicus)
External Reference Information
External Reference
UniProt:Q6AXR4
Gene Names
Hexb
Reference Genes
BioGPS Gene:294673 Hexb
ENSEMBL:ENSRNOG00000025274
ENSEMBL:ENSRNOG00000025274.7 Hexb
ENSEMBL:ENSRNOG00055028545
ENSEMBL:ENSRNOG00060028290
ENSEMBL:ENSRNOG00065022045
KEGG Gene (Rattus norvegicus):294673 Hexb
Monarch:294673 Hexb
NCBI Gene:294673 Hexb
UCSC:Q6AXR4 Hexb
Reference Transcript
RefSeq:NM_001011946.1 Hexb
Other Identifiers
10820693
1372706_at
17744528
294673
5639693
5650939
5662061
5669574
5745421
5881772
6065707
6142574
6321331
6326941
6365811
6409316
6420304
6459401
6515107
6639809
6670523
6714251
A_44_P131470
A_64_P068038
GO:0003824
GO:0004553
GO:0004563
GO:0005975
GO:0016787
ILMN_1530345
rc_AI235455_at
Participates
as a component of
Mature HEXB [lysosomal lumen] (Rattus norvegicus)
Other forms of this molecule
Hexb [extracellular region]
Hexb [extracellular region]
Hexb [azurophil granule lumen]
Hexb [azurophil granule lumen]
Hexb [lysosomal lumen]
Hexb [lysosomal lumen]
Inferred From
HEXB(316-556) [lysosomal lumen]
(Homo sapiens)
Modified Residues
Name
Inter-chain Crosslink via L-cystine (cross-link) at 360 and 309 (in Homo sapiens)
Coordinate
360
PsiMod Name
L-cystine (cross-link)
PsiMod Definition
A protein modification that effectively cross-links two L-cysteine residues to form L-cystine.
Cross References
RefSeq
NP_001011946.1
Ensembl
ENSRNOG00000025274
,
ENSRNOP00000081104
,
ENSRNOT00000097138
PRO
Q6AXR4
RGD
1307607
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