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COQ2 [mitochondrial inner membrane]
Stable Identifier
R-HSA-1299439
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Para-hydroxybenzoate--polyprenyltransferase, mitochondrial, COQ2_HUMAN
Locations in the PathwayBrowser for interactor UniProt:P36542 ATP5F1C
Expand all
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
PHB and all-E-10PrP2 are combined into DHB by COQ2 (Homo sapiens)
COQ2 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q96H96 COQ2
Gene Names
COQ2, CL640
Chain
transit peptide:1-34, chain:35-371
Reference Genes
COSMIC (genes):COQ2 COQ2
ENSEMBL:ENSG00000173085 COQ2
HGNC:25223 COQ2
OMIM:609825 COQ2
UCSC:Q96H96 COQ2
Other Identifiers
0003610184
11722311_a_at
11746747_a_at
16977520
213379_at
27235
2775966
2775967
2775968
2775973
2775975
2775978
2775979
2775980
2775981
2775982
2775988
2775989
2775990
2775991
2775992
2775993
39960_at
56599
68727
8101437
A0A1D8H0A6
CCDS47090
COQ2
COQ2-202
E2QRG7
E7EPM7
ENSG00000173085
ENSP00000310873
ENST00000311469
ENST00000311469.9
EntrezGene:27235
EntrezGene:COQ2
GE54766
GO:0002083
GO:0003674
GO:0004659
GO:0005575
GO:0005622
GO:0005623
GO:0005737
GO:0005739
GO:0005743
GO:0005975
GO:0006071
GO:0006629
GO:0006744
GO:0008150
GO:0008299
GO:0009058
GO:0016020
GO:0016021
GO:0016740
GO:0016765
GO:0031305
GO:0043226
GO:0044281
GO:0047293
GO:0051186
H0YAI0
HGNC:25223
HPA056599
HPA068727
Hs.44563.0.S2_3p_at
ILMN_1756572
IPR000537
IPR006370
IPR030470
IPR039653
MIM:146500
MIM:607426
MIM:609825
NM_015697
NP_056512
PF01040
PH_hs_0022584
TC04001346.hg
UPI0000D6158E
Participant Of
hasCandidate
Cargo of TIMM23 SORT [mitochondrial inner membrane]
Other forms of this molecule
COQ2(1-371) [mitochondrial intermembrane space]
COQ2(1-34) [mitochondrial matrix]
COQ2(1-371) [mitochondrial inner membrane]
Inferred To
COQ2 [mitochondrial inner membrane] (Bos taurus)
COQ2 [mitochondrial inner membrane] (Caenorhabditis elegans)
COQ2 [mitochondrial inner membrane] (Canis familiaris)
COQ2 [mitochondrial inner membrane] (Danio rerio)
COQ2 [mitochondrial inner membrane] (Dictyostelium discoideum)
COQ2 [mitochondrial inner membrane] (Drosophila melanogaster)
COQ2 [mitochondrial inner membrane] (Gallus gallus)
COQ2 [mitochondrial inner membrane] (Mus musculus)
COQ2 [mitochondrial inner membrane] (Plasmodium falciparum)
COQ2 [mitochondrial inner membrane] (Rattus norvegicus)
COQ2 [mitochondrial inner membrane] (Saccharomyces cerevisiae)
COQ2 [mitochondrial inner membrane] (Schizosaccharomyces pombe)
COQ2 [mitochondrial inner membrane] (Sus scrofa)
COQ2 [mitochondrial inner membrane] (Xenopus tropicalis)
Cross References
OpenTargets
ENSG00000173085
GeneCards
Q96H96
PRO
Q96H96
Orphanet
15788
HMDB Protein
HMDBP03700
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P36542 ATP5F1C
1
ATP5C1 [mitochondrial matrix]
(R-HSA-164577)
0.527
4
UniProt:P05141 SLC25A5
1
SLC25A5 [mitochondrial inner membrane]
(R-HSA-49743)
0.527
8
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